| Medullary sponge kidney associated with multivessel fibromuscular dysplasia: report of a case with renovascular hypertension. | |
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MedLine Citation:
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PMID: 18203794 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Medullary sponge kidney (MSK) is a congenital anomaly characterized by dilatation of the collecting ducts of Bellini associated with defective urinary acidification and concentration. Medullary nephrocalcinosis/ nephrolithiasis is the usual presentation in adults, however neonatal and childhood cases are being reported with increasing frequency. Among the conditions associated with MSK are Beckwith-Wiedemann syndrome/hemihyperplasia (13%), horseshoe kidney, congenital small kidney, hyperparathyroidism, Caroli syndrome, congenital hepatic fibrosis, Ehlers-Danlos syndrome, Marfan syndrome, immotile cilia syndrome, and arterial fibromuscular dysplasia. This article describes an adult female who underwent nephrectomy for renovascular hypertension due to multivessel fibromuscular dysplasia with small left kidney found to be associated with MSK. |
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Authors:
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Michele Bisceglia; Carlos Galliani |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: International journal of surgical pathology Volume: 16 ISSN: 1066-8969 ISO Abbreviation: Int. J. Surg. Pathol. Publication Date: 2008 Jan |
Date Detail:
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Created Date: 2008-01-21 Completed Date: 2008-02-20 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9314927 Medline TA: Int J Surg Pathol Country: United States |
Other Details:
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Languages: eng Pagination: 85-90 Citation Subset: IM |
Affiliation:
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Department of Pathology, IRCCS Casa Sollievo della Sofferenza Hospital, San Giovanni Rotondo, Italy. bismi@libero.it |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Female Fibromuscular Dysplasia / complications* Humans Hypertension, Renovascular / etiology*, surgery Medullary Sponge Kidney / complications*, congenital, pathology* Middle Aged Nephrectomy |
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