| Mauriac syndrome in a 3-year-old boy. | |
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MedLine Citation:
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PMID: 17360304 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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OBJECTIVE: To report a case of Mauriac syndrome in a young child with poorly controlled type 1 diabetes mellitus. METHODS: We describe the typical features of Mauriac syndrome and review the clinical, laboratory, and ultrasound findings and follow-up results in our current patient. RESULTS: Hepatomegaly, growth impairment, and cushingoid features characterize Mauriac syndrome. Most frequently, it is seen in adolescents and young adults with a history of poor glycemic control. In our current patient, a 3-year-old boy with type 1 diabetes mellitus of 2 years' duration, Mauriac syndrome developed in the context of a disrupted social environment. His liver enzyme derangement, hepatomegaly, and growth improved once euglycemia was achieved. CONCLUSION: Although Mauriac syndrome is currently uncommon, close monitoring of children with type 1 diabetes is important to maintain optimal glycemic control and prevent such an occurrence. |
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Authors:
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Shefali Mahesh; Robert J Karp; Salvador Castells; Jose Bernardo Q Quintos |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Endocrine practice : official journal of the American College of Endocrinology and the American Association of Clinical Endocrinologists Volume: 13 ISSN: 1934-2403 ISO Abbreviation: Endocr Pract Publication Date: 2007 Jan-Feb |
Date Detail:
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Created Date: 2007-03-15 Completed Date: 2007-04-12 Revised Date: 2007-10-30 |
Medline Journal Info:
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Nlm Unique ID: 9607439 Medline TA: Endocr Pract Country: United States |
Other Details:
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Languages: eng Pagination: 63-6 Citation Subset: IM |
Affiliation:
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Department of Pediatric Nephrology, Montefiore Medical Center, Bronx, New York, USA. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Child, Preschool Diabetes Mellitus, Type 1 / diagnosis*, drug therapy*, physiopathology Growth Disorders / diagnosis*, physiopathology Hepatomegaly / diagnosis*, physiopathology Humans Hyperglycemia / diagnosis, drug therapy, physiopathology Hypoglycemic Agents / therapeutic use* Insulin / therapeutic use* Male Syndrome |
| Chemical | |
Reg. No./Substance:
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0/Hypoglycemic Agents; 11061-68-0/Insulin |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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