Document Detail


Management of supravalvar aortic stenosis and severely depressed left ventricular function in a neonate with Williams syndrome.
MedLine Citation:
PMID:  19237291     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report an interesting case of a patient with Williams syndrome who presented with moderate supravalvar aortic stenosis and bilateral pulmonary artery stenosis at one week of age. The supravalvar aortic stenosis became severe by the age of one month with severe depression of left ventricular function. The patient had a difficult postoperative course, developed an acquired aortic arch hypoplasia and required multiple interventions during the first two months of life with an excellent outcome. The management of this difficult patient is discussed with focus on the importance of close follow-up, early diagnosis and early surgical intervention in improving the outcome in this difficult group of patients.
Authors:
Turki B Albacker; Darrin M Payne; Adrian Dancea; Christo Tchervenkov
Publication Detail:
Type:  Case Reports; Journal Article     Date:  2009-02-23
Journal Detail:
Title:  European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery     Volume:  35     ISSN:  1873-734X     ISO Abbreviation:  Eur J Cardiothorac Surg     Publication Date:  2009 May 
Date Detail:
Created Date:  2009-04-27     Completed Date:  2009-11-09     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8804069     Medline TA:  Eur J Cardiothorac Surg     Country:  Germany    
Other Details:
Languages:  eng     Pagination:  915-6     Citation Subset:  IM    
Affiliation:
Department of Surgery, Division of Cardiac Surgery, Montreal Children's Hospital, McGill University, Montreal, Canada. dr_turki@yahoo.com
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MeSH Terms
Descriptor/Qualifier:
Aortic Stenosis, Supravalvular / surgery*,  ultrasonography
Humans
Infant, Newborn
Ventricular Dysfunction, Left / surgery*,  ultrasonography
Williams Syndrome / surgery*,  ultrasonography

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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