Document Detail


Management and outcome of 200 cases of fetomaternal alloimmune thrombocytopenia.
MedLine Citation:
PMID:  17465957     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
BACKGROUND: Fetomaternal alloimmune thrombocytopenia (FMAIT) is the commonest cause of severe thrombocytopenia in term neonates but its management remains controversial. STUDY DESIGN AND METHODS: A 7-year prospective observational study of 200 cases of FMAIT evaluated the relationship between human platelet antigen (HPA) antibody specificity, clinical presentation, morbidity, mortality, and therapeutic interventions in the antenatal and postnatal period, with long-term follow-up of neonates with intracranial hemorrhage (ICH). RESULTS: In 1148 referrals for FMAIT, HPA antibodies were confirmed in 200 (17%). The commonest specificities were anti-HPA-1a, 150 (75%); anti-HPA-5b, 31 (15.5%); and anti-HPA-15b, 8 (4%). Of 123 (62%) cases (two sets of twins) with no previous history of FMAIT, intrauterine deaths occurred in 5: anti-HPA-1a alone, 3; in combination with anti-HPA-5b, 1; and anti-HPA-15b, 1. Of the 120 live neonates, 103 had severe thrombocytopenia and 17 (14%) developed ICH (anti-HPA-1a, 13; anti-HPA-5b, 3; anti-HPA-15b, 1). Postnatal care varied widely with 37 percent of neonates receiving random rather than HPA-1a and -5b-negative platelets. Of the remaining 77 cases with a history of FMAIT, 40 received intrauterine transfusions. Six (15%) of these fetuses died in utero and an additional 2 developed ICH postnatally. Of the 19 children with ICH, 1 (anti-HPA-15b) died on Day +1, and neurologic sequelae persist in 13 (mean follow-up, 2.5 years). CONCLUSION: HPA-1a antibodies are most commonly implicated in severe thrombocytopenia but HPA-5b and HPA-15b antibodies can also result in poor outcome. Postnatal transfusion management is extremely variable, and fetal transfusions are associated with significant morbidity and mortality.
Authors:
Cedric Ghevaert; Kate Campbell; Jill Walton; Graham A Smith; Dave Allen; Lorna M Williamson; Willem H Ouwehand; Edmund Ranasinghe
Related Documents :
16055577 - First-trimester septated cystic hygroma: prevalence, natural history, and pediatric out...
9166327 - Autosomal dominantly inherited diamond-blackfan anemia resulting in nonimmune hydrops.
21458747 - Current management of the infant who presents with neonatal encephalopathy.
21392147 - Floor mattresses: another potentially dangerous infant sleeping environment.
20658457 - Oxygen saturation in premature infants at risk for threshold retinopathy of prematurity.
6625827 - Infant feeding practices and beliefs in one community in the sierra of rural ecuador: a...
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Transfusion     Volume:  47     ISSN:  0041-1132     ISO Abbreviation:  Transfusion     Publication Date:  2007 May 
Date Detail:
Created Date:  2007-04-30     Completed Date:  2007-09-04     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0417360     Medline TA:  Transfusion     Country:  United States    
Other Details:
Languages:  eng     Pagination:  901-10     Citation Subset:  IM    
Affiliation:
National Blood Service Cambridge, Cambridge and Oxford, Department of Haematology, University of Cambridge, Cambridge, UK. cedric.ghevaert@nbs.nhs.uk
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Antigens, Human Platelet / immunology*
Blood Transfusion, Intrauterine
Female
Fetal Blood / immunology
Humans
Immunity, Maternally-Acquired / immunology*
Infant, Newborn
Isoantibodies / blood,  immunology
Isoantigens / blood,  immunology
Maternal-Fetal Exchange / immunology
Pregnancy
Pregnancy Complications, Hematologic / therapy
Prospective Studies
Thrombocytopenia / immunology*,  pathology,  therapy
Chemical
Reg. No./Substance:
0/1a alloantigen, human; 0/Antigens, Human Platelet; 0/Isoantibodies; 0/Isoantigens

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Seasonal influences on hemoglobin levels and deferral rates in whole-blood and plasma donors.
Next Document:  Fetal hemolytic anemia and intrauterine death caused by anti-M immunization.