Document Detail

Management of oesophageal stenosis in epidermolysis bullosa dystrophica.
MedLine Citation:
PMID:  2751329     Owner:  NLM     Status:  MEDLINE    
Seven patients with epidermolysis bullosa dystrophica and chronic and recurrent oesophageal lesions such as spasm, strictures, and complete occlusion were studied. Dysphagia could be cured with drugs if it was caused by bullae formation or spasm. If oesophageal strictures were present, endoscopy and bouginage with corticosteroid prophylaxis during the quiescent phase of the disease was a safe and useful procedure. We have also given corticosteroids, which reduced the oedema caused by bullae formation and oral phenytoin, which reduced epithelial detachment by inhibiting collagenase activity. Verapamil counteracted oesophageal spasm and pureed food during periods of dysphagia reduced blistering of the upper oesophagus.
I B Kern; M Eisenberg; S Willis
Related Documents :
2962609 - Radiologic quantitation of gastro-oesophageal reflux. correlation between height of foo...
18766529 - On the aetiology of intestinal intussusception in the fowl.
22221359 - Development of a pcr protocol to detect aflatoxigenic molds in food products.
22004819 - Burger preparation: what consumers say and do in the home.
22105669 - Potential biological fate of ingested nanoemulsions: influence of particle characterist...
19597009 - Food-borne trematodiases.
20933579 - Blockade of central nicotine acetylcholine receptor signaling attenuate ghrelin-induced...
2892609 - Nutritional status and energy metabolism of crayfish (procambarus clarkii, girard) musc...
22547309 - Vitamin b(12) transport from food to the body's cells-a sophisticated, multistep pathway.
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Archives of disease in childhood     Volume:  64     ISSN:  1468-2044     ISO Abbreviation:  Arch. Dis. Child.     Publication Date:  1989 Apr 
Date Detail:
Created Date:  1989-08-18     Completed Date:  1989-08-18     Revised Date:  2009-11-18    
Medline Journal Info:
Nlm Unique ID:  0372434     Medline TA:  Arch Dis Child     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  551-6     Citation Subset:  AIM; IM    
Prince of Wales Children's Hospital, Australia.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Adrenal Cortex Hormones / therapeutic use
Child, Preschool
Deglutition Disorders / etiology,  therapy
Epidermolysis Bullosa / complications*
Esophageal Stenosis / etiology,  therapy*
Phenytoin / therapeutic use
Verapamil / therapeutic use
Reg. No./Substance:
0/Adrenal Cortex Hormones; 52-53-9/Verapamil; 57-41-0/Phenytoin

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

Previous Document:  Measurement of nasal mucociliary clearance.
Next Document:  Minor congenital anomalies and ataxic cerebral palsy.