Document Detail


Management of mitochondrial stroke-like-episodes.
MedLine Citation:
PMID:  19780807     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Aim of this review is to discuss recent findings concerning the management of stroke-like episodes (SLEs) in patients with mitochondrial disorders (MIDs). Various databases were searched for appropriate literature. SLEs are a dominant feature of MIDs and occur most frequently in MELAS-syndrome, less frequently in MERRF-syndrome, Kearns-Sayre-syndrome, or Leigh-syndrome. SLEs occur at all ages and are frequently accompanied by other cerebral abnormalities. Clinically, SLEs mimic ischemic stroke but not on imaging studies and concerning the management. The morphological equivalent on MRI is the stroke-like-lesion, representing a vasogenic edema (hyperintensity on T2, diffusion-weighted imaging and apparent diffusion coefficient in the acute and subacute or chronic stage, most frequently in the parieto-occipital region, surpassing vascular territories). For diagnostic and therapeutic reasons SLEs need to be clearly delineated from ischemic stroke and cerebral bleeding. Though there is no causal therapy available, symptomatic and general measures can help to resolve the clinical manifestations. In conclusion this review shows that SLEs are a dominant feature of some syndromic or non-syndromic MIDs. The most effective strategy for the treatment of SLEs appears to be the application of L-arginine, coenzyme-Q, steroids, edaravone, creatine-monohydrate, or dichloracetate.
Authors:
J Finsterer
Related Documents :
11334377 - The diving bell meets the butterfly: identity lost and re-membered.
22285347 - Pull-through technique with pincer tactics for stent placement in severe superior vena ...
15062467 - Coagulopathy in the equine critical care patient.
176327 - Pure motor hemiplegia secondary to brain-stem tumour.
19430557 - The characteristics of acute aortic dissection among young chinese patients: a comparis...
14560117 - Multiple evanescent white dot syndrome and acute zonal occult outer retinopathies.
Publication Detail:
Type:  Journal Article; Review     Date:  2009-09-23
Journal Detail:
Title:  European journal of neurology : the official journal of the European Federation of Neurological Societies     Volume:  16     ISSN:  1468-1331     ISO Abbreviation:  Eur. J. Neurol.     Publication Date:  2009 Nov 
Date Detail:
Created Date:  2009-10-21     Completed Date:  2010-01-05     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9506311     Medline TA:  Eur J Neurol     Country:  England    
Other Details:
Languages:  eng     Pagination:  1178-84     Citation Subset:  IM    
Affiliation:
Krankenanstalt Rudolfstiftung, Vienna and Danube University, Krems, Austria. fifigs1@yahoo.de
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Brain / pathology
Brain Diseases, Metabolic, Inborn / complications,  diagnosis*,  pathology,  therapy*
Diagnosis, Differential
Humans
Magnetic Resonance Imaging
Mitochondria / pathology
Stroke / complications,  diagnosis*,  therapy*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Decision-making in Parkinson's disease patients with and without pathological gambling.
Next Document:  Independent validation of the scales for outcomes in Parkinson's disease-autonomic (SCOPA-AUT).