Document Detail


Management of cold haemolytic syndrome.
MedLine Citation:
PMID:  17561970     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Most haemolytic disease is mediated by immunoglobulin G (IgG) antibodies and leads to red blood cell destruction outside of the circulatory system. However, rare syndromes, such as paroxysmal cold haemoglobinuria, show IgG antibodies causing intravascular destruction. Haemolysis may also occur because of immunoglobulin M antibodies. Historically, these antibodies have been termed 'cold agglutinins' because they cause agglutination of red blood cells at 3 degrees C. Cold agglutinin haemolytic anaemia has been associated with a number of autoimmune and lymphoproliferative disorders, and its management differs substantially from warm antibody-mediated haemolytic anaemia. This review of cold haemolytic syndromes describes new therapies and clinical strategies to determine a correct diagnosis.
Authors:
Morie A Gertz
Publication Detail:
Type:  Journal Article; Review     Date:  2007-06-11
Journal Detail:
Title:  British journal of haematology     Volume:  138     ISSN:  0007-1048     ISO Abbreviation:  Br. J. Haematol.     Publication Date:  2007 Aug 
Date Detail:
Created Date:  2007-07-30     Completed Date:  2007-09-28     Revised Date:  2008-12-16    
Medline Journal Info:
Nlm Unique ID:  0372544     Medline TA:  Br J Haematol     Country:  England    
Other Details:
Languages:  eng     Pagination:  422-9     Citation Subset:  IM    
Affiliation:
Division of Hematology, Mayo Clinic, Rochester, MN 55905, USA. gertz.morie@mayo.edu
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MeSH Terms
Descriptor/Qualifier:
Anemia, Hemolytic, Autoimmune / drug therapy,  immunology,  therapy*
Autoantibodies / immunology
Cryoglobulins / immunology
Glucocorticoids / therapeutic use
Hemolysis
Humans
Chemical
Reg. No./Substance:
0/Autoantibodies; 0/Cryoglobulins; 0/Glucocorticoids; 0/cold agglutinins
Comments/Corrections
Comment In:
Br J Haematol. 2008 Aug;142(4):668   [PMID:  18573114 ]

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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