| Malignant hypertension in a child with phakomatosis pigmentovascularis type II b. | |
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MedLine Citation:
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PMID: 18671691 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Phakomatosis pigmentovascularis (PPV) is a rare congenital syndrome characterized predominantly by cutaneous vascular malformations and pigmentary naevi. The most frequently reported form, Type II b, is associated with systemic involvement. Sturge-Weber Syndrome (SWS) with concomitant glaucoma, Klippel-Trenaunay Syndrome (KTS) and naevus of Ota have been frequently described, but there have only been two case reports with asymptomatic renal anomalies. CONCLUSION: We report the first case of PPV associated with SWS and naevus of Ota presenting with malignant hypertension secondary to bilateral renal artery stenosis. This case raises the possibility that the phakomatoses are not distinct entities but a spectrum of overlapping neurocutaneous, vascular and renal features. |
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Authors:
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Y Kanaheswari; A H Hamzaini; S W Wong; A Zulfiqar |
Publication Detail:
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Type: Case Reports; Journal Article Date: 2008-07-29 |
Journal Detail:
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Title: Acta paediatrica (Oslo, Norway : 1992) Volume: 97 ISSN: 1651-2227 ISO Abbreviation: Acta Paediatr. Publication Date: 2008 Nov |
Date Detail:
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Created Date: 2008-10-30 Completed Date: 2008-12-30 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9205968 Medline TA: Acta Paediatr Country: Norway |
Other Details:
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Languages: eng Pagination: 1589-91 Citation Subset: IM |
Affiliation:
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Department of Paediatrics, Faculty of Medicine, Universiti Kebangsaan Malaysia, Kuala Lumpur, Malaysia. kanahes@mail.hukm.ukm.my |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Child, Preschool Female Humans Hypertension, Malignant / etiology* Infant Infant, Newborn Nevus of Ota / complications Renal Artery Obstruction / complications* Sturge-Weber Syndrome / complications* |
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