Document Detail


Macrodactyly in Proteus syndrome.
MedLine Citation:
PMID:  8345255     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A case of Proteus syndrome in a 13-year-old boy with macrodactyly, hemihypertrophy, exostosis of the skull, epidermal naevi, palmar and plantar masses, and scoliosis is reported. Macrodactyly involving the left thumb was treated surgically. The usual findings in macrodactyly, hypertrophy of the digital nerves and proliferation of subcutaneous fat, were not observed in this case. Macrodactyly associated with Proteus syndrome should be distinguished from other forms of macrodactyly because of its poor prognosis and high rate of recurrence.
Authors:
H Miura; Y Uchida; K Ihara; Y Sugioka
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of hand surgery (Edinburgh, Scotland)     Volume:  18     ISSN:  0266-7681     ISO Abbreviation:  J Hand Surg Br     Publication Date:  1993 Jun 
Date Detail:
Created Date:  1993-09-08     Completed Date:  1993-09-08     Revised Date:  2009-06-08    
Medline Journal Info:
Nlm Unique ID:  8403839     Medline TA:  J Hand Surg Br     Country:  SCOTLAND    
Other Details:
Languages:  eng     Pagination:  308-9     Citation Subset:  IM    
Affiliation:
Department of Orthopaedic Surgery, Kyushu University, Fukuoka, Japan.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Humans
Male
Proteus Syndrome* / diagnosis
Thumb / abnormalities*
Comments/Corrections
Comment In:
J Hand Surg Br. 1994 Apr;19(2):263-4   [PMID:  8014569 ]

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