Document Detail


MPPH Syndrome: Two New Cases.
MedLine Citation:
PMID:  21481746     Owner:  NLM     Status:  In-Data-Review    
Abstract/OtherAbstract:
This report describes 2 additional cases of megalencephaly and perisylvian polymicrogyria with postaxial polydactyly and hydrocephalus syndrome, a recently recognized disorder of infants and young children with macrocrania, developmental delay/mental retardation, and often epilepsy. Medulloblastoma, a previously unreported feature in megalencephaly and perisylvian polymicrogyria with postaxial polydactyly and hydrocephalus syndrome, developed in one child at 3 years of age. Although the disorder is presumed to be genetic, the cause of megalencephaly and perisylvian polymicrogyria with postaxial polydactyly and hydrocephalus syndrome has not yet been determined.
Authors:
Wendy L Osterling; Richard S Boyer; Gary L Hedlund; James F Bale
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Pediatric neurology     Volume:  44     ISSN:  1873-5150     ISO Abbreviation:  Pediatr. Neurol.     Publication Date:  2011 May 
Date Detail:
Created Date:  2011-04-12     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8508183     Medline TA:  Pediatr Neurol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  370-3     Citation Subset:  IM    
Copyright Information:
Copyright © 2011 Elsevier Inc. All rights reserved.
Affiliation:
Department of Pediatrics, the University of Utah School of Medicine, Salt Lake City, Utah, and Primary Children's Medical Center, Intermountain Healthcare Inc., Salt Lake City, Utah; Department of Neurology, the University of Utah School of Medicine, Salt Lake City, Utah, and Primary Children's Medical Center, Intermountain Healthcare Inc., Salt Lake City, Utah.
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