| Lower gastrointestinal bleeding, hematuria and splenic hemangiomas in Klippel-Trenaunay syndrome: a case report and literature review. | |
| | |
MedLine Citation:
|
PMID: 19330738 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
|
Klippel-Trenaunay syndrome is a congenital vascular anomaly characterized by a triad of varicose veins, cutaneous capillary malformation, and hypertrophy of bone and soft tissue. Gastrointestinal and genitourinary vascular malformations in Klippel- Trenaunay syndrome may present with lower gastrointestinal bleeding and hematuria. The majority of patients with splenic hemangiomatosis are asymptomatic. We herein report a case admitted to the Gastroenterology Clinic with life-threatening hematochezia and symptomatic iron deficiency anemia. The patient's history was remarkable for subtotal cystectomy and enterocystoplasty in December 2002 for vascular malformation, located in the bladder, which presented with hematuria. Although the patient was also diagnosed with colonic varices and splenic hemangiomas at that time, due to the asymptomatic mild intermittent hematochezia and splenic hemangiomas, the patient did not seek any help for rectal bleeding until her admittance to our department for evaluation of massive lower gastrointestinal bleeding. Endoscopy revealed vascular malformations starting from the transitional zone in the rectum extending up to the descending colon. Due to this extensive involvement of the rectum and sigmoid colon, no interventional endoscopic procedure was attempted and she was referred to surgery. A very low anterior resection with double stapling technique was done. Postoperative follow-up has been uneventful for six months since the operation. To the best of our knowledge, this is the first Klippel-Trenaunay syndrome case presenting with lower gastrointestinal bleeding, hematuria and splenic hemangiomas. The literature on the evaluation and management of lower gastrointestinal and genitourinary bleeding in Klippel-Trenaunay syndrome is reviewed. |
| | |
Authors:
|
Orhan Kocaman; Ahmet Alponat; Cem Aygün; Yeşim Gürbüz; H Tahsin Sarisoy; Altay Celebi; Omer Sentürk; Sadettin Hülagü |
Related Documents
:
|
5303558 - Severe gastrointestinal haemorrhage: haemangiomata demonstrated by selective visceral a... 16455548 - Cowden's syndrome with lhermitte-duclos disease. 510098 - Upper esophageal web due to a ring formed by a squamocolumnar junction with ectopic gas... 3232698 - Bleeding diathesis in noonan syndrome: a common association. 1127528 - The inheritance of the aarskog facial-digital-genital syndrome. 22111908 - Chronic granulomatous disease, the mcleod phenotype and the contiguous gene deletion sy... |
Publication Detail:
|
Type: Case Reports; Journal Article; Review |
Journal Detail:
|
Title: The Turkish journal of gastroenterology : the official journal of Turkish Society of Gastroenterology Volume: 20 ISSN: 1300-4948 ISO Abbreviation: Turk J Gastroenterol Publication Date: 2009 Mar |
Date Detail:
|
Created Date: 2009-03-30 Completed Date: 2009-05-11 Revised Date: - |
Medline Journal Info:
|
Nlm Unique ID: 9515841 Medline TA: Turk J Gastroenterol Country: Turkey |
Other Details:
|
Languages: eng Pagination: 62-6 Citation Subset: IM |
Affiliation:
|
Department of Gastroenterology, Kocaeli University, School of Medicine, Kocaeli, Turkey. drokocaman@hotmail.com |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
Female Gastrointestinal Hemorrhage / etiology*, surgery*, therapy Hemangioma / etiology* Hematuria / etiology Humans Klippel-Trenaunay-Weber Syndrome / complications*, surgery*, therapy Spleen / blood supply Vascular Neoplasms / etiology* Young Adult |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: A case of Behçet's disease presenting with massive lower gastrointestinal bleeding.
Next Document: Inferior mesenteric arteriovenous fistula with ischemic colitis: multidetector computed tomographic ...