Document Detail


Low-density lipoprotein apheresis in a pediatric patient with refractory nephrotic syndrome due to focal segmental glomerulosclerosis.
MedLine Citation:
PMID:  19444573     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Focal segmental glomerulosclerosis (FSGS) often leads to refractory nephrotic syndrome (NS). A high level of low-density lipoprotein (LDL) is a risk factor for the progression of NS. An 8-year-old girl presented with severe proteinuria refractory to steroid therapy. She was diagnosed with non-IgA diffuse mesangial proliferative glomerulonephritis. Oral prednisolone, methylprednisolone (mPL) pulse therapy, and cyclosporine and cyclophosphamide therapy failed to achieve remission. Follow-up renal biopsy revealed FSGS. Her serum level of LDL was high, and LDL-apheresis (LDL-A) was performed five times, followed by mPL pulse therapy. Urinary protein decreased from 2-4 g x day(-) to 0.5-1.0 g x day(-). LDL-A may be beneficial in the treatment of multidrug-resistant FSGS.
Authors:
Jun Oto; Kenichi Suga; Sato Matsuura; Shuji Kondo; Yoshiaki Ohnishi; Daisuke Inui; Hideaki Imanaka; Shoji Kagami; Masaji Nishimura
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2009-05-15
Journal Detail:
Title:  Journal of anesthesia     Volume:  23     ISSN:  1438-8359     ISO Abbreviation:  J Anesth     Publication Date:  2009  
Date Detail:
Created Date:  2009-05-15     Completed Date:  2009-12-07     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8905667     Medline TA:  J Anesth     Country:  Japan    
Other Details:
Languages:  eng     Pagination:  284-7     Citation Subset:  IM    
Affiliation:
Department of Emergency and Critical Care Medicine, Tokushima University Hospital, 3-18-15 Kuramoto-cho, Tokushima, 770-8503, Japan.
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MeSH Terms
Descriptor/Qualifier:
Anti-Inflammatory Agents / therapeutic use
Blood Component Removal / methods*
Child
Drug Resistance
Female
Glomerulosclerosis, Focal Segmental / complications*,  pathology
Humans
Immunosuppressive Agents / therapeutic use
Kidney / pathology
Lipoproteins, LDL / blood*
Nephrotic Syndrome / etiology*,  pathology,  therapy*
Proteinuria / etiology
Pulse Therapy, Drug
Chemical
Reg. No./Substance:
0/Anti-Inflammatory Agents; 0/Immunosuppressive Agents; 0/Lipoproteins, LDL

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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