Document Detail


Neovascularization, enhanced inflammatory response, and age-related cone dystrophy in the Nrl-/-Grk1-/- mouse retina.
MedLine Citation:
PMID:  20688726     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
PURPOSE: The effects of aging and light exposure on cone photoreceptor survival were compared between mouse retinas of neural retina leucine zipper knockout (Nrl(-/-)) mice and double-knockout mice lacking G-protein-coupled receptor kinase 1 (Nrl(-/-)Grk1(-/-)).
METHODS: Mice were reared in total darkness, ambient cyclic light, or constant light, and their retinas were evaluated from 1 to 9 months of age using immunohistochemistry, electroretinography, and fluorescein angiography. Retinal gene expression and statistically significant probe sets were categorized using analysis software. Select gene expression changes were confirmed with quantitative RT-PCR.
RESULTS: In contrast to retinas from Nrl(-/-), those from Nrl(-/-)Grk1(-/-) exhibit a progressive loss of the outer nuclear layer, retinal physiology deficits, and a higher rate of degeneration with increasing age that is independent of environmental light exposure. Changes in retinal neovascularization occur in the Nrl(-/-)Grk1(-/-) at 1 month, before the onset of significant cone functional deficits. Microarray analyses demonstrate statistically significant changes in transcript levels of more than 400 genes, of which the oncostatin M signaling pathway and the inflammatory disease response network were identified.
CONCLUSIONS: These data demonstrate that the loss of functional Grk1 on the enhanced S-cone Nrl(-/-) background exacerbates age-related cone dystrophy in a light-independent manner, mediated partly through the inflammatory response pathway and neovascularization. According to these findings, Grk1 helps to maintain a healthy cone environment, and the Nrl(-/-)Grk1(-/-) mouse allows examination of the alternative roles of Grk1 in cone photoreceptor homeostasis.
Authors:
Rosanne M Yetemian; Bruce M Brown; Cheryl M Craft
Related Documents :
8320596 - Faster than the eye can see: blue cones respond to rapid flicker.
12679876 - Visual adaptations in a diurnal rodent, octodon degus.
10708046 - Spatial summation in human cone mechanisms from 0 degrees to 20 degrees in the superior...
6980266 - Homogeneity of large-field color matches in congenital red-green color deficients.
19163976 - Wheel/tissue force interaction: a new concept for soft tissue diagnosis during mis.
22204926 - The role of haptic information in shaping coordination dynamics: inertial frame of refe...
Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't     Date:  2010-08-04
Journal Detail:
Title:  Investigative ophthalmology & visual science     Volume:  51     ISSN:  1552-5783     ISO Abbreviation:  Invest. Ophthalmol. Vis. Sci.     Publication Date:  2010 Dec 
Date Detail:
Created Date:  2010-12-02     Completed Date:  2011-01-13     Revised Date:  2011-07-28    
Medline Journal Info:
Nlm Unique ID:  7703701     Medline TA:  Invest Ophthalmol Vis Sci     Country:  United States    
Other Details:
Languages:  eng     Pagination:  6196-206     Citation Subset:  IM    
Affiliation:
Doheny Eye Institute, Department of Ophthalmology, Division of Retinal Molecular Biology, Keck School of Medicine, University of Southern California, Los Angeles, CA 90033-9224, USA.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Aging / physiology
Animals
Apoptosis
Basic-Leucine Zipper Transcription Factors / physiology*
Cell Survival
Dark Adaptation
Electroretinography
Eye Proteins / physiology*
Fluorescein Angiography
G-Protein-Coupled Receptor Kinase 1 / physiology*
Gene Silencing / physiology
Immunohistochemistry
In Situ Nick-End Labeling
Light
Mice
Mice, Inbred C57BL
Mice, Knockout
Microarray Analysis
Retinal Cone Photoreceptor Cells / pathology*,  radiation effects
Retinal Dystrophies / physiopathology*
Retinal Neovascularization / physiopathology*
Retinitis / physiopathology*
Reverse Transcriptase Polymerase Chain Reaction
Grant Support
ID/Acronym/Agency:
EY015851/EY/NEI NIH HHS; EY03040/EY/NEI NIH HHS
Chemical
Reg. No./Substance:
0/Basic-Leucine Zipper Transcription Factors; 0/Eye Proteins; 0/Nrl protein, mouse; EC 2.7.1.37/Grk1 protein, mouse; EC 2.7.11.14/G-Protein-Coupled Receptor Kinase 1
Comments/Corrections

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Effects of acutely elevated hydrostatic pressure in a rat ex vivo retinal preparation.
Next Document:  Decay accelerating factor (CD55)-mediated attenuation of complement: therapeutic implications for ag...