Document Detail


Liver transplantation in a patient with encapsulating peritoneal sclerosis.
MedLine Citation:
PMID:  18663255     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Encapsulating peritoneal sclerosis (EPS) is a poorly understood condition in which excess fibrosis results in an encasement of the small bowel, which can clinically result in obstruction. The condition is thought to be related to the persistent expression of transforming growth factor beta on mesothelial cells causing proliferation of subserosal fibroblasts, massive production of extracellular matrix and loss of mesothelial cells. We report a patient with liver cirrhosis in whom the diagnosis of EPS was made. During laparotomy for liver transplantation the complete peritoneum was found to be thickened, consisting of white sheets; liver transplantation was deferred. Histological examination showed peritoneal sclerosing fibrosis. Immunosuppressive medication was started and a difficult but successful liver transplantation followed. If EPS is diagnosed during laparotomy for organ transplantation, adjusted immunosuppression is preferred as calcineurin inhibitors such as cyclosporin and tacrolimus may accelerate EPS while prednisone and some other drugs may stop progression.
Authors:
W H de Vos Tot Nederveen Cappel; J Dubbeld; S M Willems; J Ringers; B van Hoek
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  The Netherlands journal of medicine     Volume:  66     ISSN:  0300-2977     ISO Abbreviation:  Neth J Med     Publication Date:    2008 Jul-Aug
Date Detail:
Created Date:  2008-07-29     Completed Date:  2008-09-25     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0356133     Medline TA:  Neth J Med     Country:  Netherlands    
Other Details:
Languages:  eng     Pagination:  280-2     Citation Subset:  IM    
Affiliation:
Department of Gastroenterology, Leiden University Medical Centre, the Netherlands.
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MeSH Terms
Descriptor/Qualifier:
Aged
Biopsy
Humans
Liver Cirrhosis / complications,  pathology,  surgery*
Liver Transplantation / methods*
Male
Peritoneal Diseases / complications*,  pathology,  surgery
Peritoneum / pathology*
Sclerosis / pathology,  surgery

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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