Document Detail

Liver lesion on computed tomography and ultrasonography in adult Niemann Pick disease related to sea blue histiocyte syndrome--a case report.
MedLine Citation:
PMID:  8325590     Owner:  NLM     Status:  MEDLINE    
The case of a 42-year-old man with Niemann Pick disease and a liver lesion is presented. The lesion was hypodense on CT and had mixed echogenicity on US. Hepatosplenomegaly, interstitial infiltration of the lungs, an absence of neurological signs, family history, laboratory data, sea blue histiocytes in the bone marrow and Niemann Pick's cells in the liver suggested a subtype of Niemann Pick disease (Type B), with a focal lesion in the liver due to thus condition. We believe that this is the first case in the literature. Niemann Pick disease and its subtypes, as also the sea blue histiocyte syndrome are briefly discussed.
K Strigaris; K Kokkinis; K Liberopoulos; S Kavvadias; M Tsouroulas; Z Nikolacopoulou
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Hepato-gastroenterology     Volume:  40     ISSN:  0172-6390     ISO Abbreviation:  Hepatogastroenterology     Publication Date:  1993 Jun 
Date Detail:
Created Date:  1993-08-12     Completed Date:  1993-08-12     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  8007849     Medline TA:  Hepatogastroenterology     Country:  GERMANY    
Other Details:
Languages:  eng     Pagination:  240-3     Citation Subset:  IM    
Department of Diagnostic Imaging, Peripheric General Hospital of Athens, Greece.
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MeSH Terms
Biopsy, Needle
Diagnosis, Differential
Liver / pathology*
Niemann-Pick Diseases / diagnosis*,  pathology
Sea-Blue Histiocyte Syndrome / diagnosis*,  pathology
Tomography, X-Ray Computed*

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