Document Detail


Linkage localization of the thoraco-abdominal syndrome (TAS) gene to Xq25-26.
MedLine Citation:
PMID:  7909197     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The thoraco-abdominal syndrome (TAS) presents a closure defect confined to the ventral midline, manifested as ventral hernia of various degrees in all affected individuals and antero-lateral diaphragmatic defect manifested almost exclusively in affected males. The syndrome is inherited as an X-linked dominant trait affecting blastogenesis (XLB mutation). We studied 27 members of the TAS family for linkage on the X chromosome. The best lod score of 5.5 at theta 0.04 was found for the HPRT locus on Xq26.1. A multilocus lod score of 12.4 was observed when the linkage analysis utilized additional markers in Xq25-26.
Authors:
R Parvari; Y Weinstein; S Ehrlich; M Steinitz; R Carmi
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Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  American journal of medical genetics     Volume:  49     ISSN:  0148-7299     ISO Abbreviation:  Am. J. Med. Genet.     Publication Date:  1994 Feb 
Date Detail:
Created Date:  1994-05-17     Completed Date:  1994-05-17     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  7708900     Medline TA:  Am J Med Genet     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  431-4     Citation Subset:  IM    
Affiliation:
Clinical Genetics Unit, Soroka Medical Center, Ben-Gurion University of the Negev, Beer-Sheva, Israel.
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MeSH Terms
Descriptor/Qualifier:
Abdomen / abnormalities*
Chromosome Mapping
Female
Humans
Linkage (Genetics)*
Lod Score
Male
Pedigree
Polymorphism, Restriction Fragment Length
Syndrome
Thorax / abnormalities*
X Chromosome*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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