Document Detail

Leptomeningeal angiomatosis accompanied by hair follicle nevus.
MedLine Citation:
PMID:  9660127     Owner:  NLM     Status:  MEDLINE    
A 5-day-old male infant with leptomeningeal angiomatosis accompanied by hair follicle nevus and congenital alopecia is reported. Admitted for frequent left hemiconvulsions, he had three small papular lesions around his right eye and ipsilateral alopecia from the frontal to parietal areas. Histopathological examination of the papular lesions revealed crowding of hair follicles. There were no other skin lesions and no ophthalmic abnormalities. Ictal EEG showed a theta burst in the right parietal area. Computed tomography of the brain revealed cerebral atrophy and a slightly high intensity lesion in the right parietal and occipital lobes with calcification. Gyriform enhancement was demonstrated by contrast MRI in these areas. The pathogenesis is discussed. This case may represent a previously unknown neurocutaneous syndrome.
Y Okada; K Hamano; N Iwasaki; S Iijima; I Anno
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery     Volume:  14     ISSN:  0256-7040     ISO Abbreviation:  Childs Nerv Syst     Publication Date:    1998 Apr-May
Date Detail:
Created Date:  1998-10-22     Completed Date:  1998-10-22     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  8503227     Medline TA:  Childs Nerv Syst     Country:  GERMANY    
Other Details:
Languages:  eng     Pagination:  218-21     Citation Subset:  IM    
Department of Pediatrics, Institute of Clinical Medicine, University of Tsukuba, Ibaraki, Japan.
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MeSH Terms
Alopecia / complications,  congenital
Angiomatosis / complications*,  diagnosis
Anticonvulsants / therapeutic use
Arachnoid Cysts / complications*,  diagnosis
Atrophy / complications,  pathology
Brain Diseases / complications,  diagnosis
Epilepsy / complications,  diagnosis,  drug therapy
Hair Follicle / pathology*
Infant, Newborn
Magnetic Resonance Imaging
Nevus / complications*,  diagnosis
Occipital Lobe / pathology
Parietal Lobe / pathology
Phenytoin / therapeutic use
Skin Neoplasms / complications*,  pathology
Tomography, X-Ray Computed
Reg. No./Substance:
0/Anticonvulsants; 57-41-0/Phenytoin

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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