Document Detail

Late-onset epilepsy in a surgically-treated Sturge-Weber patient.
MedLine Citation:
PMID:  19017574     Owner:  NLM     Status:  MEDLINE    
Sturge-Weber syndrome is a rare, congenital, neurocutaneous disorder. It can be associated with a variety of symptoms including severe epilepsy. Patients often become symptomatic during childhood and the severity of the epilepsy correlates with the patient's neurological outcome. The patient reported here remained asymptomatic until age 24, when he started to experience migraine accompanied by visual scotoma and hemiparesis. Ten years later, he developed severe, refractory epilepsy, with prolonged postictal neurological deficits and ictal as well as post-ictal headaches. It became increasingly difficult to distinguish between migraines and seizures as both could last for several hours, as demonstrated in the two video EEGs. Both the epilepsy and the migraine may therefore have contributed to the patient's severe, neurological deterioration, probably by accelerating the progressive neuronal damage. Surgery improved the situation, but lesional areas were too extensive for complete removal. Late-onset symptoms in Sturge-Weber syndrome may thus result in a severe course for the disease. Early intervention and surgical treatment options are discussed.
Julia Jacobs; Pierre Levan; André Olivier; Frederick Andermann; François Dubeau
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Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Epileptic disorders : international epilepsy journal with videotape     Volume:  10     ISSN:  1294-9361     ISO Abbreviation:  Epileptic Disord     Publication Date:  2008 Dec 
Date Detail:
Created Date:  2008-11-21     Completed Date:  2009-01-09     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  100891853     Medline TA:  Epileptic Disord     Country:  France    
Other Details:
Languages:  eng     Pagination:  312-8     Citation Subset:  IM    
Montreal Neurological Institute, Canada.
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MeSH Terms
Drug Resistance
Epilepsy / etiology*,  psychology,  surgery*
Migraine with Aura / etiology
Neuropsychological Tests
Neurosurgical Procedures*
Sturge-Weber Syndrome / complications*,  psychology,  surgery*

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