Document Detail

Late complication of total anomalous pulmonary venous drainage in an adult: 'a diagnostic challenge'.
MedLine Citation:
PMID:  19786890     Owner:  NLM     Status:  MEDLINE    
Total anomalous venous drainage is a rare congenital cardiac defect seen in 1% of the population; there is usually a concomitant atrial septal defect. We discuss such a diagnostic challenge in a patient who presented on a number of occasions with acute respiratory distress and haemoptysis. True understanding of her underlying congenital heart disease was not appreciated until review in a congenital heart disease clinic - in which she presented for prepregnancy counselling. She was found to have a stricture at the site of anastomosis of the common chamber with the left atrium, resulting in pulmonary venous hypertension leading to acute presentation of pulmonary haemorrhages. She underwent successful full balloon dilatation of the site, leading to full recovery. Most patients are diagnosed at birth and undergo surgical repair. The outcome is good, and historically it has been regarded that it is unusual for them to have long-term complications, although dysrhythmias remain a recognized long-term complication. Surgery for total anomalous pulmonary venous drainage is nevertheless a palliation, and it is vital that the possible role of late complications is considered in all cases.
Isma Rafiq; Leisa J Freeman; Michael Mullin
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of cardiovascular medicine (Hagerstown, Md.)     Volume:  11     ISSN:  1558-2035     ISO Abbreviation:  J Cardiovasc Med (Hagerstown)     Publication Date:  2010 Jan 
Date Detail:
Created Date:  2009-11-25     Completed Date:  2010-01-28     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101259752     Medline TA:  J Cardiovasc Med (Hagerstown)     Country:  United States    
Other Details:
Languages:  eng     Pagination:  45-8     Citation Subset:  IM    
Norfolk and Norwich University Hospital, Colney Lane, Norwich, Norfolk, UK.
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MeSH Terms
Anemia, Iron-Deficiency / etiology,  physiopathology
Balloon Dilatation
Cardiac Surgical Procedures / adverse effects*
Diagnosis, Differential
Heart Defects, Congenital / diagnosis,  physiopathology,  surgery*
Hemoptysis / etiology,  physiopathology
Hypertension, Pulmonary / diagnosis*,  etiology,  physiopathology,  therapy
Palliative Care
Preconception Care
Pulmonary Circulation*
Pulmonary Veins / abnormalities,  physiopathology,  surgery*
Respiratory Distress Syndrome, Adult / etiology,  physiopathology
Treatment Outcome
Young Adult

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