Document Detail


L-histidine decarboxylase and Tourette's syndrome.
MedLine Citation:
PMID:  20445167     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Tourette's syndrome is a common developmental neuropsychiatric disorder characterized by chronic motor and vocal tics. Despite a strong genetic contribution, inheritance is complex, and risk alleles have proven difficult to identify. Here, we describe an analysis of linkage in a two-generation pedigree leading to the identification of a rare functional mutation in the HDC gene encoding L-histidine decarboxylase, the rate-limiting enzyme in histamine biosynthesis. Our findings, together with previously published data from model systems, point to a role for histaminergic neurotransmission in the mechanism and modulation of Tourette's syndrome and tics.
Authors:
A Gulhan Ercan-Sencicek; Althea A Stillman; Ananda K Ghosh; Kaya Bilguvar; Brian J O'Roak; Christopher E Mason; Thomas Abbott; Abha Gupta; Robert A King; David L Pauls; Jay A Tischfield; Gary A Heiman; Harvey S Singer; Donald L Gilbert; Pieter J Hoekstra; Thomas M Morgan; Erin Loring; Katsuhito Yasuno; Thomas Fernandez; Stephan Sanders; Angeliki Louvi; Judy H Cho; Shrikant Mane; Christopher M Colangelo; Thomas Biederer; Richard P Lifton; Murat Gunel; Matthew W State
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Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't     Date:  2010-05-05
Journal Detail:
Title:  The New England journal of medicine     Volume:  362     ISSN:  1533-4406     ISO Abbreviation:  N. Engl. J. Med.     Publication Date:  2010 May 
Date Detail:
Created Date:  2010-05-20     Completed Date:  2010-05-27     Revised Date:  2011-09-26    
Medline Journal Info:
Nlm Unique ID:  0255562     Medline TA:  N Engl J Med     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1901-8     Citation Subset:  AIM; IM    
Copyright Information:
2010 Massachusetts Medical Society
Affiliation:
Yale University School of Medicine, New Haven, CT 06520, USA.
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MeSH Terms
Descriptor/Qualifier:
Chromosome Mapping
Codon, Nonsense*
Female
Genes, Dominant
Genetic Linkage
Genetic Predisposition to Disease
Haplotypes
Histidine Decarboxylase / genetics*,  metabolism
Humans
Male
Microsatellite Repeats
Pedigree
Polymerase Chain Reaction
Tourette Syndrome / genetics*
Grant Support
ID/Acronym/Agency:
NS016648/NS/NINDS NIH HHS; NS040024/NS/NINDS NIH HHS; R01 NS016648-29/NS/NINDS NIH HHS; R01 NS043520-05/NS/NINDS NIH HHS; R01 NS43520/NS/NINDS NIH HHS; U01 NS040024-08/NS/NINDS NIH HHS; U24 MH068457/MH/NIMH NIH HHS; U24 MH068457-07/MH/NIMH NIH HHS; U24 NS051869-02S1/NS/NINDS NIH HHS; U24 NS051869-02S1/NS/NINDS NIH HHS; UL1 RR024139/RR/NCRR NIH HHS; UL1 RR024139-04/RR/NCRR NIH HHS
Chemical
Reg. No./Substance:
0/Codon, Nonsense; EC 4.1.1.22/Histidine Decarboxylase
Comments/Corrections
Comment In:
Clin Genet. 2010 Oct;78(4):349-50   [PMID:  20718796 ]

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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