| Klippel-Trénaunay syndrome manifesting as gingival overgrowth and teeth agenesis. | |
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MedLine Citation:
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PMID: 20831140 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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OBJECTIVE: Klippel-Trénaunay syndrome (KTS) is characterized by triad of venous varicosity, naevus flammeus, and soft/hard tissue hypertrophy. Manifestations of the syndrome in the head and neck region are rare, but in some cases hemangioma of the lips, tongue, and gums, open bite and cross bite, and early tooth eruption are associated with the disease. STUDY DESIGN: We report a 12-year-old KTS patient with gingival hyperplasia, congenital missing teeth, and increased mucosal vascularization as oral manifestations. RESULTS AND CONCLUSION: All manifestations of the KTS were observed on the same side of the head, except bilateral missing teeth. Histological examination showed several vascular enlargements in enlarged gingiva. It is suggested that oral manifestations of the syndrome are generally related to the severity of the disease, but they do not always present in the same pattern. |
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Authors:
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Hakan Ozdemir; Ismail Marakoglu; Melih Akyol; O Fahrettin Goze; Ulvi Kahraman Gursoy |
Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: The Journal of clinical pediatric dentistry Volume: 34 ISSN: 1053-4628 ISO Abbreviation: J Clin Pediatr Dent Publication Date: 2010 |
Date Detail:
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Created Date: 2010-09-13 Completed Date: 2010-11-02 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9100079 Medline TA: J Clin Pediatr Dent Country: United States |
Other Details:
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Languages: eng Pagination: 351-4 Citation Subset: D |
Affiliation:
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Department of Periodontology, Cumhuriyet University, Sivas, Turkey. hozdemir@cumhuriyet.edu.tr |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Anodontia
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pathology* Bicuspid / abnormalities Capillaries / pathology Child Epithelial Cells / pathology Gingiva / blood supply Gingival Overgrowth / pathology* Humans Hypertrophy Klippel-Trenaunay-Weber Syndrome / pathology* Lip / blood supply, pathology Male Plasma Cells / pathology |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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