| Klippel-Trénaunay syndrome: 2 case reports and a review of genitourinary manifestations. | |
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MedLine Citation:
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PMID: 11547101 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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PURPOSE: We summarize the literature and present our experience with genitourinary manifestations of the Klippel-Trénaunay syndrome, which can lead to challenging management problems. MATERIALS AND METHODS: We report on 2 patients with genitourinary manifestations of the Klippel-Trénaunay syndrome and performed a MEDLINE review of the literature using the key words "Klippel-Trénaunay," "vascular malformation" and "genitourinary." RESULTS: Genitourinary manifestations were cited in 18 articles, including 1,174 cases of the Klippel-Trénaunay syndrome, detailing the presentation and management of bladder, external genitalia and retroperitoneal involvement in the Klippel-Trénaunay syndrome. The overall genitourinary symptoms in patients with the Klippel-Trénaunay syndrome seem to occur in the more severe cases and usually involve cutaneous vascular malformations of the trunk, pelvis and genitalia. CONCLUSIONS: Intra-abdominal and intrapelvic extension of the vascular malformations of the Klippel-Trénaunay syndrome frequently occurs concurrently with the lower abdominal, pelvic cutaneous involvement of the external genitalia, as in our 2 cases and in our review of the literature. These data provide a better understanding of the spectrum of genitourinary manifestations in the Klippel-Trénaunay syndrome and provide insight for the clinician to formulate individual therapies for these patients. |
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Authors:
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P D Furness; A Z Barqawi; G Bisignani; R M Decter |
Publication Detail:
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Type: Case Reports; Journal Article; Review |
Journal Detail:
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Title: The Journal of urology Volume: 166 ISSN: 0022-5347 ISO Abbreviation: J. Urol. Publication Date: 2001 Oct |
Date Detail:
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Created Date: 2001-09-07 Completed Date: 2001-12-04 Revised Date: 2006-11-15 |
Medline Journal Info:
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Nlm Unique ID: 0376374 Medline TA: J Urol Country: United States |
Other Details:
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Languages: eng Pagination: 1418-20 Citation Subset: AIM; IM |
Affiliation:
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Department of Pediatric Urology, Childrens Hospital and University of Colorado Health Science Center, Denver, Colorado, USA. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Humans Infant Infant, Newborn Klippel-Trenaunay-Weber Syndrome / complications, diagnosis* Male Male Urogenital Diseases / etiology* |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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