| Klippel-Trenaunay syndrome and cerebral haemangiopericytoma: a potential association. | |
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MedLine Citation:
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PMID: 18297229 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Klippel-Trenaunay syndrome (KTS) a rare mesodermal phakomatosis consisting of capillary malformations, varicose veins, and limb hypertrophy, often associated with vascular malformations and benign tumours. A 33-year-old male presented with headaches secondary to a previously diagnosed intracranial tumour. He had a large blanching port-wine stain and hypertrophy of the left side of his body and limbs partial syndactyly of the 2(nd) and 3(rd) digits in all four extremities. The lesion was surgically resected and histology showed a Haemangiopericytoma. Thus KTS may be associated with intracranial Haemangiopericytomas, a malignant vascular tumour. |
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Authors:
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M S Mathews; R C Kim; G Y Chang; M E Linskey |
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Publication Detail:
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Type: Case Reports; Journal Article Date: 2008-02-25 |
Journal Detail:
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Title: Acta neurochirurgica Volume: 150 ISSN: 0942-0940 ISO Abbreviation: Acta Neurochir (Wien) Publication Date: 2008 Apr |
Date Detail:
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Created Date: 2008-03-17 Completed Date: 2008-04-14 Revised Date: 2009-11-11 |
Medline Journal Info:
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Nlm Unique ID: 0151000 Medline TA: Acta Neurochir (Wien) Country: Austria |
Other Details:
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Languages: eng Pagination: 399-402; discussion 402 Citation Subset: IM |
Affiliation:
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Department of Neurological Surgery, University of California Irvine, Orange, CA, USA. mmathews@uci.edu |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adult Combined Modality Therapy Dura Mater* / pathology Hemangiopericytoma / diagnosis*, pathology, therapy Humans Klippel-Trenaunay-Weber Syndrome / diagnosis*, pathology, therapy Magnetic Resonance Imaging Male Meningeal Neoplasms / diagnosis*, pathology, therapy Nerve Compression Syndromes / diagnosis, pathology, therapy Neurologic Examination Optic Nerve Diseases / diagnosis, pathology, surgery Tomography, X-Ray Computed |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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