| Klippel-Trenaunay and Sturge-Weber syndromes with renal hemangioma and double inferior vena cava. | |
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MedLine Citation:
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PMID: 3016342 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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We describe a 3 1/2-year-old boy with the Klippel-Trenaunay and Sturge-Weber syndromes. The child had congenital superficial capillary hemangiomas, congenital glaucoma and mild hydrocephalus. During the first year of life he experienced intermittent hematuria. When he was 3 years old he presented with seizures and left hemihypertrophy first was noted. Several months later radiological examination of a large abdominal mass demonstrated its origin to be in the right kidney. Radical nephrectomy documented the presence of renal hemangioma with complicating perirenal hematoma. A double inferior vena cava was another unexpected surgical finding that complicated the course of this patient. All of these unusual features in these rare syndromes with their clinical, pathogenetic and therapeutic implications are discussed. The differential diagnosis of renal masses in these syndromes also is presented. |
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Authors:
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D Schofield; G S Zaatari; B B Gay |
Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: The Journal of urology Volume: 136 ISSN: 0022-5347 ISO Abbreviation: J. Urol. Publication Date: 1986 Aug |
Date Detail:
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Created Date: 1986-09-17 Completed Date: 1986-09-17 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 0376374 Medline TA: J Urol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 442-5 Citation Subset: AIM; IM |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Angiomatosis
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complications* Child, Preschool Glaucoma / congenital Hemangioma / complications*, pathology Humans Hydrocephalus / complications Kidney / pathology Kidney Neoplasms / complications*, pathology Klippel-Trenaunay-Weber Syndrome / complications* Male Skin Neoplasms / complications Sturge-Weber Syndrome / complications* Vena Cava, Inferior / abnormalities* |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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