| Klippel-Feil syndrome revisited: diagnostic pitfalls impacting neurosurgical management. | |
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MedLine Citation:
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PMID: 1394279 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Klippel-Feil syndrome in its most basic definition includes several anomalous conditions of the cervicomedullary junction and suboccipital region. Pediatric neurosurgeons are often involved in surgical palliation of this syndrome, without realizing how the accompanying anomalies may obfuscate management in the older child. A brief review of the embryology of the rhombencephalon helps to clarify the etiology of some of these symptoms which may cause confusion and, occasionally, inappropriate treatment. Illustrative cases will demonstrate some of these pitfalls. Appropriate early intervention, such as posterior fossa decompression, ventricular shunting, and fundal plication, may help to avoid needless morbidity. The advent of magnetic resonance scanning has helped to clarify the diagnosis and resulted in more appropriate treatment in these cases. |
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Authors:
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M C Johnson |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery Volume: 8 ISSN: 0256-7040 ISO Abbreviation: Childs Nerv Syst Publication Date: 1992 Sep |
Date Detail:
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Created Date: 1992-11-23 Completed Date: 1992-11-23 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 8503227 Medline TA: Childs Nerv Syst Country: GERMANY |
Other Details:
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Languages: eng Pagination: 322-5 Citation Subset: IM |
Affiliation:
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Division of Pediatric Neurosurgery, Children's Health Care Center, Emanuel Hospital, Portland, OR 97227. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Female Humans Infant, Newborn Klippel-Feil Syndrome / diagnosis*, surgery* Magnetic Resonance Imaging Male Neurosurgery Postoperative Complications |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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