Document Detail


Klippel-Feil syndrome associated with malformed larynx. Case report.
MedLine Citation:
PMID:  8122836     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report a case of a 45-year-old man with Klippel-Feil syndrome with fusion of the C2-3 and C4-5 cervical vertebrae and severe voice impairment associated with malformation of the laryngeal cartilages. The condition was also complicated by bilateral inflexibility of the arms and legs and external malformation of the ears. This case broadens the spectrum of anomalies, of branchial arch derivation, now identified in association with Klippel-Feil syndrome. We discuss the possibility that perturbation of segmentation, distinct from somitogenesis, may be linked to Klippel-Feil syndrome-associated craniofacial abnormalities.
Authors:
R A Clarke; P J Davis; J Tonkin
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  The Annals of otology, rhinology, and laryngology     Volume:  103     ISSN:  0003-4894     ISO Abbreviation:  Ann. Otol. Rhinol. Laryngol.     Publication Date:  1994 Mar 
Date Detail:
Created Date:  1994-04-06     Completed Date:  1994-04-06     Revised Date:  2006-05-15    
Medline Journal Info:
Nlm Unique ID:  0407300     Medline TA:  Ann Otol Rhinol Laryngol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  201-7     Citation Subset:  AIM; IM    
Affiliation:
School of Biochemistry and Molecular Genetics, University of New South Wales, Kensington, Australia.
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MeSH Terms
Descriptor/Qualifier:
Humans
Klippel-Feil Syndrome / complications,  pathology*,  physiopathology
Laryngeal Cartilages / abnormalities
Larynx / abnormalities*,  physiopathology
Male
Middle Aged
Voice Disorders / etiology*,  physiopathology

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