Document Detail


Kabuki syndrome and cancer in two patients.
MedLine Citation:
PMID:  20503331     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Both hepatoblastoma and neuroblastoma are occasionally associated with congenital syndromes such as Beckwith-Wiedemann syndrome and trisomy 18. There have been no reports of hepatoblastoma in patients with Kabuki syndrome, whereas one patient with neuroblastoma and this syndrome has been reported. In this paper we present two patients with Kabuki syndrome and a neoplasm: a child of 6 years with hepatoblastoma and an infant, of 6 months affected by neuroblastoma.
Authors:
Manuela Tumino; Maria Licciardello; Giovanni Sorge; Maria Concetta Cutrupi; Fabrizio Di Benedetto; Loredana Amoroso; Roberta Catania; Monica Pennisi; Salvatore D'Amico; Andrea Di Cataldo
Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  American journal of medical genetics. Part A     Volume:  152A     ISSN:  1552-4833     ISO Abbreviation:  Am. J. Med. Genet. A     Publication Date:  2010 Jun 
Date Detail:
Created Date:  2010-05-26     Completed Date:  2010-08-30     Revised Date:  2011-07-11    
Medline Journal Info:
Nlm Unique ID:  101235741     Medline TA:  Am J Med Genet A     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1536-9     Citation Subset:  IM    
Copyright Information:
(c) 2010 Wiley-Liss, Inc.
Affiliation:
Unit of Pediatric Hematology/Oncology, Department of Pediatrics, University of Catania, Catania, Italy.
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / diagnosis*,  genetics
Adrenal Gland Neoplasms / diagnosis*,  genetics,  radiography
Child
Facies*
Female
Hepatoblastoma / diagnosis*,  genetics
Humans
Infant
Liver Neoplasms / diagnosis*,  genetics
Male
Mental Retardation / diagnosis*,  genetics
Neuroblastoma / diagnosis*,  genetics,  radiography
Syndrome
Comments/Corrections
Comment In:
Am J Med Genet A. 2011 Jun;155A(6):1504   [PMID:  21548020 ]

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