Document Detail


KID syndrome associated with features of ichthyosis hystrix.
MedLine Citation:
PMID:  10792799     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Keratitis-ichthyosis-deafness (KID) syndrome is a congenital ectodermal disorder causing erythrokeratoderma, vascularizing keratitis, and neurosensory deafness. Ichthyosis hystrix is a rare cutaneous disease characterized by well-demarcated, spiky, verrucous, linear plaques that is believed to be a clinical and pathologic chimera of two autosomal dominant diseases: epidermal nevus and epidermolytic hyperkeratosis. We present a patient with the classic triad of KID syndrome with clinical and histologic features of ichthyosis hystrix. This case demonstrates that KID syndrome comprises a spectrum of ectodermal disorders which may include diseases such as hystrix ichthyosis and deafness (HID) syndrome.
Authors:
H C Nousari; A Kimyai-Asadi; J L Pinto
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric dermatology     Volume:  17     ISSN:  0736-8046     ISO Abbreviation:  Pediatr Dermatol     Publication Date:    2000 Mar-Apr
Date Detail:
Created Date:  2000-07-13     Completed Date:  2000-07-13     Revised Date:  2009-03-03    
Medline Journal Info:
Nlm Unique ID:  8406799     Medline TA:  Pediatr Dermatol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  115-7     Citation Subset:  IM    
Affiliation:
Department of Dermatology, Johns Hopkins Medical Institutions, Baltimore, Maryland 21205, USA. hnousari@welchlink.welch.jhu.edu
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MeSH Terms
Descriptor/Qualifier:
Argentina
Biopsy, Needle
Child
Deafness*
Humans
Ichthyosis Vulgaris / diagnosis*,  pathology
Keratitis / diagnosis*
Male
Prognosis
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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