Document Detail

Juvenile idiopathic fibrosing pancreatitis.
MedLine Citation:
PMID:  12064796     Owner:  NLM     Status:  MEDLINE    
Chronic pancreatitis is a rare differential diagnosis of obstructive jaundice and/or recurrent abdominal pain in childhood and adolescence. The hereditary calcifying and the noncalcifying obstructive form are the two major forms of juvenile chronic pancreatitis. Other causes include cystic fibrosis, hyperparathyroidism, hyperlipoproteinemia and ascariasis. Even less common is the so called idiopathic or fibrosing pancreatitis. Since the first description by Comfort in 1946 only 41 further cases of juvenile idiopathic fibrosing pancreatitis have been published. An association with gene mutations (PRSS1, SPINK1, CTFR-5T genotype) is suspected. We report the cases of a 17-year-old male patient who presented with painless obstructive jaundice and a 16-year-old female patient who presented with abdominal pain and obstructive jaundice. Both patients underwent surgical treatment with duodenum-preserving pancreatic head resection. The relevant literature with special regard to modern pancreatic surgery is reviewed to give an overview about this rare but surgically treatable pediatric condition, which merits the attention of pediatricians and gastroenterologists in cases of children and adolescents suffering from unexplained abdominal pain.
Guido Sclabas; Timo Kirschstein; Waldemar Uhl; Rainer Hürlimann; Charles Ruchti; Markus W Büchler
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Digestive diseases and sciences     Volume:  47     ISSN:  0163-2116     ISO Abbreviation:  Dig. Dis. Sci.     Publication Date:  2002 Jun 
Date Detail:
Created Date:  2002-06-14     Completed Date:  2002-06-25     Revised Date:  2005-11-16    
Medline Journal Info:
Nlm Unique ID:  7902782     Medline TA:  Dig Dis Sci     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1230-5     Citation Subset:  AIM; IM    
Department of Visceral and Transplantation Surgery, University of Berne, Switzerland.
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MeSH Terms
Abdominal Pain / etiology
Cholestasis / etiology
Chronic Disease
Pancreas / pathology,  radiography
Pancreatitis / diagnosis*,  pathology,  radiography,  surgery*

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