Document Detail


Jaffe-Campanacci syndrome: case report and review of literature.
MedLine Citation:
PMID:  7894737     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report a 27-year-old Caucasian woman with Jaffe-Campanacci syndrome. She presented with multiple café-au-lait spots and multiple non-ossifying fibromata of the bones, noted on radiographs and proven by tissue biopsies. Only the left side was involved. She also suffered from moderate scoliosis, stenosis of the aortic isthmus, chylothorax, and a chylopericardium. The etiology is discussed.
Authors:
D Kotzot; H Stöss; H Wagner; R Ulmer
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Clinical dysmorphology     Volume:  3     ISSN:  0962-8827     ISO Abbreviation:  Clin. Dysmorphol.     Publication Date:  1994 Oct 
Date Detail:
Created Date:  1995-04-27     Completed Date:  1995-04-27     Revised Date:  2005-11-16    
Medline Journal Info:
Nlm Unique ID:  9207893     Medline TA:  Clin Dysmorphol     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  328-34     Citation Subset:  IM    
Affiliation:
Institute of Human Genetics, University of Erlangen-Nürnberg, Germany.
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MeSH Terms
Descriptor/Qualifier:
Adult
Aortic Valve Stenosis / diagnosis*
Biopsy
Bone Neoplasms / pathology*,  radiography
Chylothorax / diagnosis*
Female
Fibroma / pathology*,  radiography
Humans
Male
Pericardial Effusion / diagnosis*
Scoliosis / radiography*
Skin Diseases / pathology*
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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