Document Detail


Isolated thrombocytopenia in children: thinking beyond idiopathic thrombocytopenic purpura and leukaemia.
MedLine Citation:
PMID:  18036021     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The commonest cause of isolated thrombocytopenia in an otherwise well child is idiopathic thrombocytopenic purpura (ITP). The inherited thrombocytopenias such as Bernard-Soulier syndrome are rare but often misdiagnosed as ITP owing to a similar clinical presentation. We describe a child with Bernard-Soulier syndrome who presented with isolated thrombocytopenia, mimicking ITP. Features which help to differentiate these two conditions are discussed with a brief literature review.
Authors:
Radhakrishnan Kottayam; Gillian Rozenberg; Tim Brighton; Richard J Cohn
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Journal of paediatrics and child health     Volume:  43     ISSN:  1034-4810     ISO Abbreviation:  J Paediatr Child Health     Publication Date:  2007 Dec 
Date Detail:
Created Date:  2007-11-26     Completed Date:  2008-02-14     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9005421     Medline TA:  J Paediatr Child Health     Country:  Australia    
Other Details:
Languages:  eng     Pagination:  848-50     Citation Subset:  IM    
Affiliation:
Centre for Children's Cancer and Blood Disorders, Sydney Children's Hospital, Randwick, New South Wales, Australia.
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MeSH Terms
Descriptor/Qualifier:
Bernard-Soulier Syndrome / physiopathology*
Child, Preschool
Diagnosis, Differential
Humans
Leukemia / diagnosis*
Male
New South Wales
Thrombocytopenia / diagnosis*,  etiology

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