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Isolated left ventricular noncompaction: a review of three different presentations for a rare disease.
MedLine Citation:
PMID:  23427367     Owner:  NLM     Status:  In-Process    
Abstract/OtherAbstract:
Isolated left ventricular noncompaction (ILVNC) is a rare cardiomyopathy with a genetic background characterized by numerous prominent trabeculations and deep intertrabecular recesses. It occurs in the absence of any coexisting congenital lesion or hemodynamic abnormality and is rare in the adult population. Heart failure, ventricular arrhythmias, and embolic events are the three major clinical manifestations of ILVNC. Medical and surgical treatment is similar to other systolic dysfunction cardiomyopathies and depends on the presenting clinical manifestations. In this review, we present three patients with different clinical presentations of ILVNC leading to different treatment modalities ranging from medications alone to device implantation and transplantation. Pathologic findings from one of our patients are also presented.
Authors:
Marcos Amuchástegui; Tomas Amuchastegui; Alejandro Ernesto Contreras; Marcos Amuchástegui; Thomas Donohue; Andre Ghantous
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Connecticut medicine     Volume:  77     ISSN:  0010-6178     ISO Abbreviation:  Conn Med     Publication Date:  2013 Jan 
Date Detail:
Created Date:  2013-02-22     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0372745     Medline TA:  Conn Med     Country:  United States    
Other Details:
Languages:  eng     Pagination:  11-8     Citation Subset:  IM    
Affiliation:
Yale New Haven Hospital, St. Raphael Campus Department of Medicine, Section of Cardiology, New Haven, USA.
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