Document Detail


Intranasal insulin to improve developmental delay in children with 22q13 deletion syndrome: an exploratory clinical trial.
MedLine Citation:
PMID:  18948358     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
BACKGROUND: The 22q13 deletion syndrome (Phelan-McDermid syndrome) is characterised by a global developmental delay, absent or delayed speech, generalised hypotonia, autistic behaviour and characteristic phenotypic features. Intranasal insulin has been shown to improve declarative memory in healthy adult subjects and in patients with Alzheimer disease. AIMS: To assess if intranasal insulin is also able to improve the developmental delay in children with 22q13 deletion syndrome. METHODS: We performed exploratory clinical trials in six children with 22q13 deletion syndrome who received intranasal insulin over a period of 1 year. Short-term (during the first 6 weeks) and long-term effects (after 12 months of treatment) on motor skills, cognitive functions, or autonomous functions, speech and communication, emotional state, social behaviour, behavioural disorders, independence in daily living and education were assessed. RESULTS: The children showed marked short-term improvements in gross and fine motor activities, cognitive functions and educational level. Positive long-term effects were found for fine and gross motor activities, nonverbal communication, cognitive functions and autonomy. Possible side effects were found in one patient who displayed changes in balance, extreme sensitivity to touch and general loss of interest. One patient complained of intermittent nose bleeding. CONCLUSIONS: We conclude that long-term administration of intranasal insulin may benefit motor development, cognitive functions and spontaneous activity in children with 22q13 deletion syndrome.
Authors:
H Schmidt; W Kern; R Giese; M Hallschmid; A Enders
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Publication Detail:
Type:  Clinical Trial; Journal Article     Date:  2008-10-23
Journal Detail:
Title:  Journal of medical genetics     Volume:  46     ISSN:  1468-6244     ISO Abbreviation:  J. Med. Genet.     Publication Date:  2009 Apr 
Date Detail:
Created Date:  2009-04-09     Completed Date:  2009-05-28     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  2985087R     Medline TA:  J Med Genet     Country:  England    
Other Details:
Languages:  eng     Pagination:  217-22     Citation Subset:  IM    
Affiliation:
Dr von Hauner Children's Hospital, University of Munich, Lindwurmstr. 4, 80337 Munich, Germany. heinrich.schmidt@med.uni-muenchen.de
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MeSH Terms
Descriptor/Qualifier:
Administration, Intranasal
Child
Child, Preschool
Chromosome Deletion*
Chromosome Disorders / drug therapy,  genetics,  pathology
Chromosomes, Human, Pair 22 / genetics*
Cognition / drug effects
Developmental Disabilities / drug therapy*,  genetics,  pathology
Female
Humans
Hypoglycemic Agents / administration & dosage,  therapeutic use
Infant
Insulin / administration & dosage,  therapeutic use*
Male
Motor Skills / drug effects
Syndrome
Time Factors
Treatment Outcome
Chemical
Reg. No./Substance:
0/Hypoglycemic Agents; 11061-68-0/Insulin

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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