Document Detail


Interleukin-13 (IL-13)/IL-13 receptor alpha1 (IL-13Ralpha1) signaling regulates intestinal epithelial cystic fibrosis transmembrane conductance regulator channel-dependent Cl- secretion.
MedLine Citation:
PMID:  21303908     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Interleukin-13 (IL-13) has been linked to the pathogenesis of inflammatory diseases of the gastrointestinal tract. It is postulated that IL-13 drives inflammatory lesions through the modulation of both hematopoietic and nonhematopoietic cell function in the intestine. To delineate the relevant contribution of elevated levels of intestinal IL-13 to intestinal structure and function, we generated an intestinal IL-13 transgenic mouse (iIL-13Tg). We show that constitutive overexpression of IL-13 in the small bowel induces modification of intestinal epithelial architecture (villus blunting, goblet cell hyperplasia, and increased epithelial proliferation) and epithelial function (altered basolateral → apical Cl(-) ion conductance). Pharmacological analyses in vitro and in vivo determined that elevated Cl(-) conductance is mediated by altered cystic fibrosis transmembrane conductance regulator expression and activity. Generation of iIL-13Tg/Il13rα1(-/-), iIL-13Tg/Il13rα2(-/-), and iIL-13Tg/Stat6(-/-) mice revealed that IL-13-mediated dysregulation of epithelial architecture and Cl(-) conductance is dependent on IL-13Rα1 and STAT-6. These observations demonstrate a central role for the IL-13/IL-13Rα1 pathway in the regulation of intestinal epithelial cell Cl(-) secretion via up-regulation of cystic fibrosis transmembrane conductance regulator, suggesting an important role for this pathway in secretory diarrhea.
Authors:
David Wu; Richard Ahrens; Heather Osterfeld; Taeko K Noah; Katherine Groschwitz; Paul S Foster; Kris A Steinbrecher; Marc E Rothenberg; Noah F Shroyer; Klaus I Matthaei; Fred D Finkelman; Simon P Hogan
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Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, Non-P.H.S.     Date:  2011-02-08
Journal Detail:
Title:  The Journal of biological chemistry     Volume:  286     ISSN:  1083-351X     ISO Abbreviation:  J. Biol. Chem.     Publication Date:  2011 Apr 
Date Detail:
Created Date:  2011-04-11     Completed Date:  2011-06-28     Revised Date:  2012-04-16    
Medline Journal Info:
Nlm Unique ID:  2985121R     Medline TA:  J Biol Chem     Country:  United States    
Other Details:
Languages:  eng     Pagination:  13357-69     Citation Subset:  IM    
Affiliation:
Division of Allergy and Immunology, Department of Pediatrics, Cincinnati Children's Hospital Medical Center, University of Cincinnati College of Medicine, Cincinnati, Ohio 45229, USA.
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MeSH Terms
Descriptor/Qualifier:
Animals
Caco-2 Cells
Chlorides / metabolism*
Cystic Fibrosis Transmembrane Conductance Regulator / genetics,  metabolism*
Cysts / genetics,  metabolism,  pathology
Diarrhea / genetics,  metabolism,  pathology
Fibrosis
Humans
Interleukin-13 / genetics,  metabolism*
Interleukin-13 Receptor alpha1 Subunit / genetics,  metabolism*
Intestinal Diseases / genetics,  metabolism*,  pathology
Intestinal Mucosa / metabolism*,  pathology
Ion Transport / genetics
Mice
Mice, Inbred BALB C
Mice, Knockout
STAT6 Transcription Factor / genetics,  metabolism
Grant Support
ID/Acronym/Agency:
R01 CA142826-01/CA/NCI NIH HHS; R01AI073553-01/AI/NIAID NIH HHS; R03 DK084167-01/DK/NIDDK NIH HHS
Chemical
Reg. No./Substance:
0/Chlorides; 0/Il13ra1 protein, mouse; 0/Interleukin-13; 0/Interleukin-13 Receptor alpha1 Subunit; 0/STAT6 Transcription Factor; 0/Stat6 protein, mouse; 126880-72-6/Cystic Fibrosis Transmembrane Conductance Regulator

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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