Document Detail


Incidence of mosaic cell lines in vivo and malsegregation of chromosome 21 in lymphocytes in vitro of trisomy 21 patients: detection by fluorescence in situ hybridization on binucleated lymphocytes.
MedLine Citation:
PMID:  10982178     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
In order to detect aneuploidy in interphase human lymphocytes, both in vivo and in vitro, fluorescence in situ hybridization (FISH) was carried out on binucleated cells cytokinesis-blocked by cytochalasin B at the first mitosis after phytohemagglutinin stimulation. A pericentric chromosome-21-specific DNA probe prepared from yeast artificial chromosome clone 881D2 by the polymerase chain reaction was employed. One thousand binucleated cells per individual were scored from cultures from twelve trisomy 21 patients aged 0.01-8.9 years (mean 4.3 years) and 20 normal children of similar age. Of trisomy 21 patients, increased frequencies of disomic cells in vivo (1.690+/-1.070%) and cells containing six signals with nondisjunction (0.822+/-0.554%) were found, compared with those of monosomic 21 cells in vivo (0.265+/-0.130%) and cells containing four signals with nondisjunction in normal children (0.369+/-0.250%; P=0.000 and P=0.000, respectively). These results show that malsegregation of chromosome 21 occurs more often in trisomic 21 cells than in disomic cells from normal children. The frequency of nondisjunction was significantly higher than the loss of chromosome 21 in both cultured trisomic (0.822+/-0.554% vs 0.043+/-0.049%, P=0.000) and disomic (0.369+/-0.250% vs 0.010+/-0.30%, P=0.000) cells. Comparisons of in vivo and in vitro data on aneuploidy indicate that a cell selection mechanism may exist in vivo. All these results show that FISH, with a chromosome-specific probe, on binucleated lymphocytes is a powerful tool for simultaneously detecting mosaic cell lines in vivo and malsegregation (loss and nondisjunction) of a corresponding chromosome in vitro in the same cell population.
Authors:
Q Shi; I D Adler; J Zhang; X Zhang; X Shan; R Martin
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Human genetics     Volume:  106     ISSN:  0340-6717     ISO Abbreviation:  Hum. Genet.     Publication Date:  2000 Jan 
Date Detail:
Created Date:  2000-09-22     Completed Date:  2000-09-22     Revised Date:  2006-04-06    
Medline Journal Info:
Nlm Unique ID:  7613873     Medline TA:  Hum Genet     Country:  GERMANY    
Other Details:
Languages:  eng     Pagination:  29-35     Citation Subset:  IM    
Affiliation:
Institut für Säugetiergenetik, GSF Forschungszentrum für Umwelt und Gesundheit, Neuherberg, Germany. qshi@ucalgary.ca
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MeSH Terms
Descriptor/Qualifier:
Case-Control Studies
Cell Division / genetics
Cell Line
Centromere / ultrastructure
Child
Child, Preschool
Chromosome Segregation*
Chromosomes, Artificial, Yeast
Chromosomes, Human, Pair 21*
Down Syndrome / genetics*
Female
Genetic Markers
Humans
In Situ Hybridization, Fluorescence
Infant
Infant, Newborn
Lymphocytes / ultrastructure
Male
Models, Genetic
Mosaicism*
Polymerase Chain Reaction
Chemical
Reg. No./Substance:
0/Genetic Markers

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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