Document Detail


In utero central nervous system damage in pyruvate dehydrogenase deficiency.
MedLine Citation:
PMID:  3137916     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Pyruvate dehydrogenase deficiency is among the most common causes of congenital lactic acidosis. We describe siblings with congenital lactic acidosis due to a deficiency of pyruvate dehydrogenase complex. The findings of computed tomography and pathologic studies suggest that central nervous system damage had occurred in utero. These observations have implications for treatment and outcome in patients with enzymatic defects causing congenital lactic acidosis.
Authors:
K A Aleck; A M Kaplan; W G Sherwood; B H Robinson
Related Documents :
15728286 - The neuropathology of hereditary congenital facial palsy vs möbius syndrome.
8408706 - Acute myelomonocytic leukaemia following atypical congenital rubella.
2910286 - Ocular manifestations of the congenital varicella syndrome.
16586236 - Adams-oliver syndrome associated with cutis marmorata telangiectatica congenita and con...
16441466 - Systematic review: complementary and alternative medicine in the irritable bowel syndrome.
7277426 - Asplenia and polysplenia syndromes with abnormalities of lateralisation in a sibship.
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Archives of neurology     Volume:  45     ISSN:  0003-9942     ISO Abbreviation:  Arch. Neurol.     Publication Date:  1988 Sep 
Date Detail:
Created Date:  1988-09-29     Completed Date:  1988-09-29     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  0372436     Medline TA:  Arch Neurol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  987-9     Citation Subset:  AIM; IM    
Affiliation:
Department of Pediatrics, Phoenix Children's Hospital, AZ 85006.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Brain / embryology,  pathology*,  radiography
Female
Fetal Diseases / genetics,  pathology*,  radiography
Fetus / anatomy & histology
Humans
Infant, Newborn
Ketoglutarate Dehydrogenase Complex / metabolism
Male
Pregnancy
Pyruvate Dehydrogenase Complex / metabolism
Pyruvate Dehydrogenase Complex Deficiency Disease*
Tomography, X-Ray Computed
Chemical
Reg. No./Substance:
0/Pyruvate Dehydrogenase Complex; EC 1.2.4.2/Ketoglutarate Dehydrogenase Complex

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Lithium-induced downbeat nystagmus.
Next Document:  Body composition research at the University of Auckland--some implications for modern surgical pract...