Document Detail


Improved respiratory prognosis in patients with cystic fibrosis with normal fat absorption.
MedLine Citation:
PMID:  7086584     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The clinical presentation, courses, and sweat chloride values of 72 CF patients with normal fat absorption are described. In general, these patients had milder clinical symptoms and a lower mean sweat chloride value than their counterparts with steatorrhoea. Pulmonary function tests, including FEV1, FVC, FEF25%-75%, PaO2, and RV/TLC%, were significantly better in patients with normal fat absorption compared with both male and female patients who had steatorrhoea. The maintenance of better pulmonary function, coupled with the low mortality, suggests that patients without steatorrhoea have a better prognosis. This difference remains unexplained, but may be contributed to by nutritional, genetic, or pancreatic factors.
Authors:
K Gaskin; D Gurwitz; P Durie; M Corey; H Levison; G Forstner
Related Documents :
12142724 - Beta2 adrenoceptor gene polymorphisms in cystic fibrosis lung disease.
9061354 - Serum igg response to an outer membrane porin protein of burkholderia cepacia in patien...
8849704 - Persistence of staphylococcus aureus strains among cystic fibrosis patients over extend...
8169414 - Immunization of noncolonized cystic fibrosis patients against pseudomonas aeruginosa.
22849354 - The role of tocilizumab in the management of rheumatoid arthritis.
20374314 - Human leucocyte antigen-b27 subtypes in korean patients with ankylosing spondylitis: hi...
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  The Journal of pediatrics     Volume:  100     ISSN:  0022-3476     ISO Abbreviation:  J. Pediatr.     Publication Date:  1982 Jun 
Date Detail:
Created Date:  1982-08-26     Completed Date:  1982-08-26     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  0375410     Medline TA:  J Pediatr     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  857-62     Citation Subset:  AIM; IM    
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Child
Child, Preschool
Chlorides / analysis
Cystic Fibrosis / metabolism,  physiopathology*
Dietary Fats / metabolism*
Female
Humans
Infant
Intestinal Absorption
Male
Pancreas / physiopathology
Prognosis
Respiration*
Respiratory Function Tests
Sex Factors
Sweat / analysis
Chemical
Reg. No./Substance:
0/Chlorides; 0/Dietary Fats

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  The response of isolated rat heart cells to cardiotoxic concentrations of isoprenaline.
Next Document:  Pneumothorax in cystic fibrosis: management and outcome.