Document Detail


Impaired oxidative metabolism in exercising muscle from ALS patients.
MedLine Citation:
PMID:  11676993     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The pathogenic mechanism of selective loss of motor neurones in amyotrophic lateral sclerosis (ALS) is still poorly understood. Recently, research evidence has suggested that mitochondrial dysfunction occurs in central nervous system as well as in peripheral tissues from ALS patients. The aim of our study was to indirectly investigate in vivo oxidative metabolism of exercising muscle in a case history of patients affected by ALS. To this purpose 11 patients, 8 male and 3 female, mean age+/-SD: 52.4+/-11.1 years, performed a bicycle incremental test for the assessment of lactate production. At rest, there was increased lactate concentration in patients: 2.77+/-0.79 vs. 1.48+/-0.49 mmol/l in normal controls (normal range: 0.67-2.47 mmol/l). Analysis of lactate curve during exercise showed a lactate production increase compared to controls. Furthermore, anaerobic lactate threshold was detected at 40-50% of the predicted normal power output, anticipated with respect to both normal subjects and non-ALS chronically denervated controls with comparable motor impairment (60-70%), suggesting that mitochondrial dysfunction can occur in exercising skeletal muscle from ALS patients.
Authors:
G Siciliano; E Pastorini; L Pasquali; M L Manca; A Iudice; L Murri
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Publication Detail:
Type:  Clinical Trial; Comparative Study; Controlled Clinical Trial; Journal Article    
Journal Detail:
Title:  Journal of the neurological sciences     Volume:  191     ISSN:  0022-510X     ISO Abbreviation:  J. Neurol. Sci.     Publication Date:  2001 Oct 
Date Detail:
Created Date:  2001-10-25     Completed Date:  2002-01-30     Revised Date:  2008-11-21    
Medline Journal Info:
Nlm Unique ID:  0375403     Medline TA:  J Neurol Sci     Country:  Netherlands    
Other Details:
Languages:  eng     Pagination:  61-5     Citation Subset:  IM    
Affiliation:
Neurological Clinics, Department of Neuroscience, University of Pisa, Via Roma 67, 56126, Pisa, Italy. gsicilia@med.unipi.it
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MeSH Terms
Descriptor/Qualifier:
Adult
Aged
Amyotrophic Lateral Sclerosis / physiopathology*
Electromyography
Exercise Test
Female
Heart Rate
Humans
Lactic Acid / blood
Male
Middle Aged
Mitochondria / metabolism
Muscle, Skeletal / physiopathology*
Neuromuscular Diseases / physiopathology
Oxidation-Reduction
Oximetry
Oxygen Consumption
Physical Exertion*
Reference Values
Chemical
Reg. No./Substance:
50-21-5/Lactic Acid

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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