Document Detail


Identification of known and novel PTCH mutations in both syndromic and non-syndromic keratocystic odontogenic tumors.
MedLine Citation:
PMID:  20690502     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
AIM: To clarify the role of PTCH in patients with NBCCS-related and non-sydromic keratocystic odontogenic tumors. METHODOLOGY: Mutation analysis was undertaken in 8 sporadic and 4 NBCCS-associated KCOTs. RESULTS: Four novel and two known mutations were identified in 2 sporadic and 3 syndromic cases, two of which being germline mutations (c.2179delT, c.2824delC) and 4 somatic mutations (c.3162dupG, c.1362-1374dup, c.1012 C>T, c.403C>T). CONCLUSION: Our findings suggest that defects of PTCH are associated with the pathogenesis of syndromic as well as a subset of non-syndromic KCOTs.
Authors:
Shuang Pan; Li-li Xu; Li-sha Sun; Tie-jun Li
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  International journal of oral science     Volume:  1     ISSN:  1674-2818     ISO Abbreviation:  Int J Oral Sci     Publication Date:  2009 Mar 
Date Detail:
Created Date:  2010-08-09     Completed Date:  2010-09-14     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101504351     Medline TA:  Int J Oral Sci     Country:  China    
Other Details:
Languages:  eng     Pagination:  34-8     Citation Subset:  D; IM    
Affiliation:
Department of Oral Pathology, Peking University School and Hospital of Stomatology, Beijing, China.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Amino Acid Sequence
Basal Cell Nevus Syndrome / genetics*
Chromatography, High Pressure Liquid
Codon, Nonsense / genetics
Codon, Terminator / genetics
Conserved Sequence / genetics
Cytosine
Exons / genetics
Female
Frameshift Mutation / genetics
Gene Duplication
Germ-Line Mutation / genetics
Guanine
Humans
Male
Middle Aged
Mutation / genetics*
Mutation, Missense / genetics
Odontogenic Tumors / genetics*
Receptors, Cell Surface / genetics*
Reverse Transcriptase Polymerase Chain Reaction
Sequence Deletion / genetics
Syndrome
Threonine / genetics
Thymine
Chemical
Reg. No./Substance:
0/Codon, Nonsense; 0/Codon, Terminator; 0/Receptors, Cell Surface; 0/patched receptors; 65-71-4/Thymine; 71-30-7/Cytosine; 72-19-5/Threonine; 73-40-5/Guanine

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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