Document Detail


Hypertrichosis terminalis, gingival hyperplasia, and a characteristic face: a new distinct entity.
MedLine Citation:
PMID:  12503107     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Congenital generalized hypertrichosis terminalis has been described in association with other features as gingival hyperplasia, osteochondrodysplasia, and a dysmorphic face. Bondeson and Miles [1993: Am J Med Genet 47:198-212] described a woman with universal congenital hypertrichosis terminalis associated with gingival hyperplasia; the face of this patient was coarse and different from other forms of hypertrichosis described before. We present an 11-year, 6-month-old girl with universal congenital hypertrichosis terminalis, gingival hyperplasia, and a characteristic coarse face resembling the patient described by Bondeson and Miles [1993: Am J Med Genet 47:198-212]. We propose that this type of congenital generalized hypertrichosis terminalis, associated with gingival hyperplasia and a coarse face, is a distinctive new entity.
Authors:
Sonia Canún; E G Guevara-Sanginés; A Elvira-Morales; Ma del C Sierra-Romero; H Rodríguez-Asbun
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  American journal of medical genetics. Part A     Volume:  116A     ISSN:  1552-4825     ISO Abbreviation:  Am. J. Med. Genet. A     Publication Date:  2003 Jan 
Date Detail:
Created Date:  2002-12-27     Completed Date:  2003-04-30     Revised Date:  2008-05-21    
Medline Journal Info:
Nlm Unique ID:  101235741     Medline TA:  Am J Med Genet A     Country:  United States    
Other Details:
Languages:  eng     Pagination:  278-83     Citation Subset:  IM    
Copyright Information:
Copyright 2002 Wiley-Liss, Inc.
Affiliation:
División de Genética, Hospital General Dr. Manuel Gea González, México City, México. scanuns@hotmail.com
Data Bank Information
Bank Name/Acc. No.:
OMIM/135400;  145700;  145701;  307150
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / genetics,  pathology*
Child
Face / abnormalities*
Female
Gingival Hyperplasia / pathology*
Humans
Hypertrichosis / pathology*
Infant
Karyotyping

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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