Document Detail

Hyperostotic macrodactyly and lipofibromatous hamartoma of the median nerve associated with carpal tunnel syndrome.
MedLine Citation:
PMID:  10855329     Owner:  NLM     Status:  MEDLINE    
A new case with 14-year follow-up of an extremely rare variety of congenital hand macrodactyly is presented. The disease characteristically presents a diffuse proliferation of fibrofatty tissue, but in this special type, osteocartilaginous deposits around the joints can also be found. The case presented included the troublesome feature of a lipofibromatous hamartoma in the median nerve at the wrist and its branches producing carpal tunnel syndrome. The patient obtained benefit from carpal tunnel release and epineurolysis. The hyperostotic development was managed with conservative resection of the periarticular osteochondromas. The literature reviewed suggests that the hyperostotic cases of macrodactyly do not differ from general cases of this congenital condition, except for the osteochondral deposits. These tumours develop during adulthood or after previous trauma, before epiphyseal closure.
A Nogueira; C Pena; M J Martinez; J G Sarasua; B Madrigal
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Chirurgie de la main     Volume:  18     ISSN:  1297-3203     ISO Abbreviation:  Chir Main     Publication Date:  1999  
Date Detail:
Created Date:  2000-07-06     Completed Date:  2000-07-06     Revised Date:  2005-11-16    
Medline Journal Info:
Nlm Unique ID:  100937750     Medline TA:  Chir Main     Country:  FRANCE    
Other Details:
Languages:  eng     Pagination:  261-71     Citation Subset:  IM    
Department of Plastic Surgery, Hospital Central de Asturias, Oviedo, Spain.
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MeSH Terms
Adipose Tissue / pathology
Bone Neoplasms / complications
Carpal Tunnel Syndrome / etiology*
Finger Joint / pathology
Fingers / abnormalities*
Follow-Up Studies
Hamartoma / complications*,  pathology
Hyperostosis / complications*
Joint Diseases / complications
Median Neuropathy / complications*,  pathology
Osteochondroma / complications

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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