Document Detail


Human RECQ helicases: roles in DNA metabolism, mutagenesis and cancer biology.
MedLine Citation:
PMID:  20934517     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Helicases use the energy of ATP hydrolysis to separate double-stranded nucleic acids to facilitate essential processes such as replication, recombination, transcription and repair. This article focuses on the human RECQ helicase gene and protein family. Loss of function of three different members has been shown to cause Bloom syndrome (BS), Werner syndrome (WS) and Rothmund-Thomson syndrome (RTS). This article outlines clinical and cellular features of these cancer predisposition syndromes, and discusses their pathogenesis in light of our understanding of RECQ helicase biochemical activities and in vivo functions. I also discuss the emerging role for RECQ helicases as predictors of disease risk and the response to therapy.
Authors:
Raymond J Monnat
Related Documents :
10812037 - Psychiatric disorders and mutations at the wolfram syndrome locus.
14648217 - Further delineation of the congenital form of x-linked dyskeratosis congenita (hoyeraal...
15245427 - A phenotype resembling the clouston syndrome with deafness is associated with a novel m...
3087197 - Chromosome findings in the rett syndrome and a test of a two-step mutation theory.
8946117 - Short rib-polydactyly syndrome in twins: beemer-langer type with polydactyly.
482177 - Thyrotoxicosis as a mimic of dementia and/or stroke-like syndrome.
Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Review     Date:  2010-10-08
Journal Detail:
Title:  Seminars in cancer biology     Volume:  20     ISSN:  1096-3650     ISO Abbreviation:  Semin. Cancer Biol.     Publication Date:  2010 Oct 
Date Detail:
Created Date:  2010-11-29     Completed Date:  2011-03-24     Revised Date:  2012-05-07    
Medline Journal Info:
Nlm Unique ID:  9010218     Medline TA:  Semin Cancer Biol     Country:  England    
Other Details:
Languages:  eng     Pagination:  329-39     Citation Subset:  IM    
Copyright Information:
Copyright © 2010 Elsevier Ltd. All rights reserved.
Affiliation:
Department of Pathology, University of Washington, Seattle, WA 98195-7705, USA. monnat@u.washington.edu
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Bloom Syndrome / genetics
DNA / genetics,  metabolism*
DNA Repair
DNA Replication
Genomic Instability
Humans
Mutagenesis*
Mutation
Neoplasms / genetics*
RecQ Helicases / genetics*,  metabolism*
Rothmund-Thomson Syndrome / genetics
Telomere
Werner Syndrome / genetics
Grant Support
ID/Acronym/Agency:
P01 CA077852-13/CA/NCI NIH HHS
Chemical
Reg. No./Substance:
9007-49-2/DNA; EC 3.6.1.-/RecQ Helicases
Comments/Corrections

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Mutator phenotypes due to DNA replication infidelity.
Next Document:  Aberrant expression of alternative DNA polymerases: a source of mutator phenotype as well as replica...