| How we approach peripheral pulmonary stenosis in Williams-Beuren syndrome. | |
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MedLine Citation:
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PMID: 19349025 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Williams-Beuren syndrome is associated with supravalvar aortic stenosis and peripheral pulmonary artery stenosis in the majority of affected individuals. Among patients in whom surgery for supravalvar aortic stenosis is contemplated, stenosis of the branch pulmonary arteries is common. For asymptomatic patients with subsystemic right ventricular pressure, the natural history is favorable and no intervention is necessary. For patients with important proximal branch pulmonary artery, stenoses patch arterioplasty can be accomplished at the time of surgery for supravalvar aortic stenosis. For patients with important peripheral pulmonary stenosis, preoperative catheter-based therapy is indicated. Surgical repair of peripheral pulmonary stenosis is indicated when preoperative intervention is unsuccessful and can include a combination of patch arterioplasty as well as intraoperative application of catheter-based techniques. This report will address the approach to this lesion with catheter-based approaches, surgical approaches, and their combination. |
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Authors:
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Kim L Gandy; James S Tweddell; Andrew N Pelech |
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Publication Detail:
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Type: Journal Article |
Journal Detail:
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Title: Seminars in thoracic and cardiovascular surgery. Pediatric cardiac surgery annual Volume: - ISSN: 1092-9126 ISO Abbreviation: Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu Publication Date: 2009 |
Date Detail:
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Created Date: 2009-04-07 Completed Date: 2009-07-29 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9815944 Medline TA: Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu Country: United States |
Other Details:
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Languages: eng Pagination: 118-21 Citation Subset: IM |
Affiliation:
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Department of Surgery, Division of Cardiothoracic Surgery, The Medical College of Wisconsin, USA. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Cardiac Surgical Procedures
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methods* Humans Pulmonary Valve Stenosis / physiopathology, surgery* Williams Syndrome / physiopathology, surgery* |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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