Document Detail


High-speed, ultrahigh resolution optical coherence tomography of the retina in Hunter syndrome.
MedLine Citation:
PMID:  17955852     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A 42-year-old man with Hunter syndrome developed bilateral visual field loss. Visual field testing demon-strated bilateral ring scotomata that corresponded to areas of thinning seen on standard resolution optical coherence tomography. High-speed, ultrahigh resolution optical coherence tomography, capable of 3.5-micron axial resolution, showed a loss of photoreceptors outside the fovea and cystoid spaces within the inner nuclear, ganglion cell, and outer nuclear layers. These results were consistent with histopathologic features that have been reported previously in patients with Hunter syndrome. Optical coherence tomography could be used as a diagnostic modality to monitor patients with Hunter syndrome and to detect subclinical forms of disease.
Authors:
Michael K Yoon; Royce W Chen; Thomas R Hedges; Vivek J Srinivasan; Iwona Gorczynska; James G Fujimoto; Maciej Wojtkowski; Joel S Schuman; Jay S Duker
Publication Detail:
Type:  Case Reports; Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, Non-P.H.S.    
Journal Detail:
Title:  Ophthalmic surgery, lasers & imaging : the official journal of the International Society for Imaging in the Eye     Volume:  38     ISSN:  1542-8877     ISO Abbreviation:  Ophthalmic Surg Lasers Imaging     Publication Date:    2007 Sep-Oct
Date Detail:
Created Date:  2007-10-24     Completed Date:  2007-11-13     Revised Date:  2011-05-05    
Medline Journal Info:
Nlm Unique ID:  101155780     Medline TA:  Ophthalmic Surg Lasers Imaging     Country:  United States    
Other Details:
Languages:  eng     Pagination:  423-8     Citation Subset:  IM    
Affiliation:
New England Eye Center, Tufts-New England Medical Center, Tufts University, Boston, Massachusetts 02111, USA.
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MeSH Terms
Descriptor/Qualifier:
Adult
Fluorescein Angiography
Fundus Oculi
Humans
Male
Mucopolysaccharidosis II / diagnosis*,  physiopathology
Optic Disk / pathology
Tomography, Optical Coherence / methods*
Visual Field Tests
Visual Fields
Grant Support
ID/Acronym/Agency:
P30 EY008098-20/EY/NEI NIH HHS; P30 EY013078-05/EY/NEI NIH HHS; R01 EY011289-20/EY/NEI NIH HHS; R01 EY013178-07/EY/NEI NIH HHS; R01-EY13178-06/EY/NEI NIH HHS
Comments/Corrections

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