| Hemangioma of the radius associated with Kasabach-Merritt syndrome: case report and literature review. | |
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MedLine Citation:
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PMID: 14676541 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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The Kasabach-Merritt syndrome of consumptive coagulopathy associated with massive hemangiomas is a potentially life-threatening problem in patients with a pathologic fracture of the osseous lesion. This can result in massive bleeding even after minor trauma. In such patients, operative management of long bone hemangiomatous lesions, including percutaneous needle aspirations, may be contraindicated, and nonoperative management may be preferable. Kasabach-Merritt syndrome must be suspected in patients with large hemangiomas with associated bone lesions, and appropriate coagulation studies should be obtained before any operative management. Review of the world English literature on Kasabach-Merritt syndrome has revealed that the most common pathologic fractures occur in the vertebral bodies. An additional case report of a child with a pathologic fracture and deformity of his radius has been documented. Decreased hematocrit and fibrinogen levels associated with thrombocytopenia and a prolonged prothrombin time and partial thromboplastin time in association with bone hemangioma should alert the orthopaedist to the possibility of Kasabach-Merritt syndrome. |
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Authors:
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Iftikhar A Mukhtar; Merv Letts |
Publication Detail:
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Type: Case Reports; Journal Article; Review |
Journal Detail:
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Title: Journal of pediatric orthopedics Volume: 24 ISSN: 0271-6798 ISO Abbreviation: J Pediatr Orthop Publication Date: 2004 Jan-Feb |
Date Detail:
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Created Date: 2003-12-16 Completed Date: 2004-04-23 Revised Date: 2005-11-16 |
Medline Journal Info:
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Nlm Unique ID: 8109053 Medline TA: J Pediatr Orthop Country: United States |
Other Details:
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Languages: eng Pagination: 87-91 Citation Subset: IM |
Affiliation:
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Division of Orthopedic Surgery, Children's Hospital of Eastern Ontario, Ottawa, Canada. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Bone Neoplasms / complications*, radiography Disseminated Intravascular Coagulation / complications* Fractures, Spontaneous / complications* Hemangioma / complications*, radiography Humans Magnetic Resonance Imaging Male Radius* Syndrome |
| Comments/Corrections | |
Comment In:
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J Pediatr Orthop. 2004 Jul-Aug;24(4):450
[PMID:
15205633
]
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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