| Hearing loss in the cervico-oculo-acoustic (Wildervanck) syndrome. | |
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MedLine Citation:
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PMID: 6689909 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A 22-year-old woman with mixed hearing loss, Klippel-Feil anomalad (fused cervical vertebrae), and bilateral abducens palsy with retracted bulb (Duane's syndrome) is classified as having the cervico-oculo-acoustic syndrome or Wildervanck syndrome. In this syndrome, the unilateral or bilateral congenital hearing loss is usually severe and of neurosensory origin. To our knowledge, this is the third case of this syndrome with the classical triad and a mixed hearing loss. It is the second case in which an exploratory tympanotomy was performed. An ankylosis of the stapes was found. Stapedectomy and Teflon interposition were successfully carried out. Since the triad of the cervico-oculo-acoustic syndrome can be incomplete, a review of the association of Klippel-Feil anomalad and hearing loss is also presented, with special attention to the anomalies of the ossicular chain. |
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Authors:
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C W Cremers; G A Hoogland; W Kuypers |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Archives of otolaryngology (Chicago, Ill. : 1960) Volume: 110 ISSN: 0003-9977 ISO Abbreviation: Arch Otolaryngol Publication Date: 1984 Jan |
Date Detail:
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Created Date: 1984-01-26 Completed Date: 1984-01-26 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 0376526 Medline TA: Arch Otolaryngol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 54-7 Citation Subset: AIM; IM |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Adult Child Female Hearing Loss / diagnosis* Hearing Loss, Conductive / congenital, diagnosis*, surgery Humans Klippel-Feil Syndrome / diagnosis* Male Ophthalmoplegia / diagnosis* Syndrome |
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