Document Detail


Guidelines for the diagnosis of fragile X syndrome. National Fragile X Foundation.
MedLine Citation:
PMID:  8100582     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Direct DNA analysis of the fragile X mutation has become available with the isolation of DNA probes that detect the unstable DNA sequence containing the CGG repeat. We present the various alternatives of combinations of probes and enzymes that can be used for the diagnosis of fragile X syndrome. An overview is given of all the different available probes. A different protocol is presented for postnatal and prenatal diagnosis of fragile X syndrome. This includes Southern blot analysis as well as direct analysis of the CGG repeat by PCR amplification. We discuss the role of constitutional cytogenetic analysis in the diagnosis of mentally retarded subjects and cytogenetic analysis for the diagnosis of fragile X syndrome.
Authors:
B A Oostra; P B Jacky; W T Brown; F Rousseau
Publication Detail:
Type:  Guideline; Journal Article; Practice Guideline    
Journal Detail:
Title:  Journal of medical genetics     Volume:  30     ISSN:  0022-2593     ISO Abbreviation:  J. Med. Genet.     Publication Date:  1993 May 
Date Detail:
Created Date:  1993-08-05     Completed Date:  1993-08-05     Revised Date:  2010-09-13    
Medline Journal Info:
Nlm Unique ID:  2985087R     Medline TA:  J Med Genet     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  410-3     Citation Subset:  IM    
Affiliation:
Department of Cell Biology, Erasmus University, Rotterdam, The Netherlands.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adult
Blotting, Southern
DNA / analysis
DNA Probes / diagnostic use
Female
Fragile X Syndrome / diagnosis*
Humans
Infant
Male
Polymerase Chain Reaction
Polymorphism, Restriction Fragment Length
Pregnancy
Prenatal Diagnosis
Repetitive Sequences, Nucleic Acid
Restriction Mapping
Chemical
Reg. No./Substance:
0/DNA Probes; 9007-49-2/DNA
Comments/Corrections

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Familial amyloidotic polyneuropathy in Sweden: a pedigree analysis.
Next Document:  Effect of the histamine antagonist cimetidine on infarct size in the rat.