Document Detail


Graves' disease and stiff-person (stiff-man) syndrome: case report and literature review.
MedLine Citation:
PMID:  16006304     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
OBJECTIVE: To report an association between two autoimmune conditions, Graves' disease and stiff-person (stiff-man) syndrome, and discuss the relevant literature. METHODS: We present a case of a 52-year-old white woman with stiff-person syndrome who also had Graves' disease, discuss her management, and review the related literature. Pertinent published reports from 1950 through 2004 were researched with use of MEDLINE and PubMed, and cross-references to other articles were reviewed. RESULTS: A 52-year-old white woman presented with symptoms of hyperthyroidism due to Graves' disease. Laboratory data were as follows: thyrotropin <0.005 m IU/mL, thyroxine 11.1 microg/dL, free thyroxine index (FTI) 10.7, and triiodothyronine 170 ng/dL. Thyroid-stimulating immunoglobulins (TSI) and thyrotropin-binding inhibitory immunoglobulins (TBII) were positive at 1,986% and 82.5 U/L, respectively. The hyperthyroidism was treated with propranolol. She had a long-standing history of musculoskeletal complaints and was ultimately diagnosed with stiff-person syndrome. During her thyroid evaluation, she had severe neurologic deterioration that necessitated hospitalization and treatment with clonazepam, baclofen, intravenous immunoglobulin, and subsequently prednisone and azathioprine for appreciable symptomatic relief. The aggressive immunosuppression had a profound effect on her symptoms of hyperthyroidism, results of thyroid function tests, and thyrotropin receptor antibodies (TRABs). Thyrotropin was 0.52 microIU/mL, thyroxine was 6.9 microg/dL, and FTI was 5.7. The TSI decreased from 1,986% to 248%, and her TBII normalized from 82.5 U/L to <5 U/L. She was clinically and biochemically euthyroid at last follow-up in May 2004. CONCLUSION: This case illustrates the association between TRAB-positive Graves' disease and stiff-person syndrome and the improvement of Graves' disease with immunosuppressive therapy.
Authors:
Israel B Orija; Manjula Gupta; Robert S Zimmerman
Related Documents :
7674004 - Chronic tonsillar herniation in crouzon's and apert's syndromes: the role of premature ...
6224294 - Down's syndrome in adults: brain metabolism.
10807714 - Oral manifestations of patients with turner syndrome.
20379824 - Occipital expansion without osteotomies in apert syndrome.
18830624 - Acute febrile neutrophilic dermatosis (sweet's syndrome) in childhood and adolescence: ...
3115194 - Collagen biosynthesis and isomorphism in a case of ehlers-danlos syndrome type vi.
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Endocrine practice : official journal of the American College of Endocrinology and the American Association of Clinical Endocrinologists     Volume:  11     ISSN:  1530-891X     ISO Abbreviation:  Endocr Pract     Publication Date:    2005 Jul-Aug
Date Detail:
Created Date:  2005-07-11     Completed Date:  2006-01-03     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9607439     Medline TA:  Endocr Pract     Country:  United States    
Other Details:
Languages:  eng     Pagination:  259-64     Citation Subset:  IM    
Affiliation:
Atlanta Medical Center, Atlanta, Georgia 30312-1212, USA.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Female
Graves Disease / complications*,  diagnosis,  drug therapy
Humans
Immunosuppressive Agents / therapeutic use
Middle Aged
Stiff-Person Syndrome / complications*,  diagnosis,  drug therapy
Chemical
Reg. No./Substance:
0/Immunosuppressive Agents

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Impending cardiac tamponade as a primary presentation of hypothyroidism: case report and review of l...
Next Document:  Higher-level mechanisms detect facial symmetry.