Document Detail

Giant stomach secondary to juvenile polyposis syndrome.
MedLine Citation:
PMID:  22005895     Owner:  NLM     Status:  MEDLINE    
INTRODUCTION: Juvenile polyposis syndrome (JPS) is a rare, autosomal dominant condition. The polyps predominate in the colon but may be seen less commonly in the stomach or small intestine. We report an unusual case of JPS associated with massive gastric polyposis, resulting in a giant stomach, severe anemia, hematemesis, protein-losing enteropathy, and gastric outlet obstruction. Progressive complications ultimately necessitated a total gastrectomy.
CASE: A 27-year-old woman presented in 2005 with severe anemia. Gastroscopy revealed severe gastric polyposis. Histopathology confirmed juvenile polyposis. Gastrectomy was initially declined. Progressive hematemesis, hypoproteinemia, and gastric outlet obstruction, however, resulted in a total gastrectomy 5 years following initial presentation. Massive gastric polyposis resulted in severe gastromegaly.
Nathalie Wong-Chong; Wondwossen Hailu Kidanewold; Richard Kirsch; Gary Robert May; Judith Andrea McCart
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2011-10-18
Journal Detail:
Title:  Journal of gastrointestinal surgery : official journal of the Society for Surgery of the Alimentary Tract     Volume:  16     ISSN:  1873-4626     ISO Abbreviation:  J. Gastrointest. Surg.     Publication Date:  2012 Mar 
Date Detail:
Created Date:  2012-02-08     Completed Date:  2012-07-10     Revised Date:  2013-05-20    
Medline Journal Info:
Nlm Unique ID:  9706084     Medline TA:  J Gastrointest Surg     Country:  United States    
Other Details:
Languages:  eng     Pagination:  669-72     Citation Subset:  IM    
Department of Surgery, Mount Sinai Hospital, 600 University Avenue, Suite 1225, Toronto, ON, M5G 1X5, Canada.
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MeSH Terms
Diagnosis, Differential
Follow-Up Studies
Intestinal Polyposis / complications,  congenital*,  diagnosis
Neoplastic Syndromes, Hereditary
Stomach Diseases / diagnosis,  etiology*,  surgery

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