Document Detail


Gastrointestinal involvement in tuberous sclerosis. Two case reports.
MedLine Citation:
PMID:  7930433     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Two patients with tuberous sclerosis had multiple semispherical polyps in the large intestine, predominantly in the rectosigmoid colon. These were hamartomas with an excess of smooth muscle fibers in the stroma. In addition, the 21-year-old man had multiple tiny protrusions in the esophagus and oral fibroepithelial polyps. In the 31-year-old woman, who had pulmonary lymphangiomyomatosis with positive estrogen and progesterone receptors, hamartomatous gastric polyps, colonic leiomyoma, and adenomatous rectal polyps were also identified. Our findings suggest that gastrointestinal polyposis may be one of the phenotypes of tuberous sclerosis complex, possibly linking this disease with other hereditary polyposis syndromes.
Authors:
K Hizawa; M Iida; T Matsumoto; M Tominaga; C Hirota; T Yao; M Fujishima
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of clinical gastroenterology     Volume:  19     ISSN:  0192-0790     ISO Abbreviation:  J. Clin. Gastroenterol.     Publication Date:  1994 Jul 
Date Detail:
Created Date:  1994-11-04     Completed Date:  1994-11-04     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  7910017     Medline TA:  J Clin Gastroenterol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  46-9     Citation Subset:  IM    
Affiliation:
Second Department of Internal Medicine, Faculty of Medicine, Kyushu University, Fukuoka, Japan.
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MeSH Terms
Descriptor/Qualifier:
Adult
Colonoscopy
Digestive System / pathology,  radiography
Endoscopy, Gastrointestinal
Female
Gastrointestinal Diseases / diagnosis*
Humans
Male
Tuberous Sclerosis / diagnosis*

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